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当代埃布斯坦畸形的管理:一个胎儿的故事及多方协作——病例报告

Management of Ebstein Anomaly in the Current Era: The Story of One Fetus and the Collaboration of Many-A Case Report.

作者信息

Kavanaugh-McHugh Ann, Zuckerwise Lisa C, Killen Stacy A S, Morris Emily A, Sullivan Rachel T, Alrifai Mhd Wael, Bichell David P, Smith-Parrish Melissa, Freud Lindsay

机构信息

Thomas. P. Graham Jr. Division of Pediatric Cardiology, Department of Pediatrics, Monroe Carell Jr. Children's Hospital at Vanderbilt, Vanderbilt University Medical Center, Nashville, TN 37232, USA.

Division of Maternal-Fetal Medicine, Department of Obstetrics and Gynecology, University of Virginia School of Medicine, Charlottesville, VA 22908, USA.

出版信息

J Cardiovasc Dev Dis. 2024 May 9;11(5):147. doi: 10.3390/jcdd11050147.

DOI:10.3390/jcdd11050147
PMID:38786969
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC11122070/
Abstract

Collaborative multicenter research has significantly increased our understanding of fetal Ebstein anomaly, delineating risk factors for adverse outcomes as well as predictors of postnatal management. These data are incorporated into prenatal care and therapeutic strategies and inform family counseling and delivery planning to optimize care. This report details the translation of findings from multicenter studies into multidisciplinary prenatal care for a fetus with Ebstein anomaly, supraventricular tachycardia, and a circular shunt, including transplacental therapy to control arrhythmias and achieve ductal constriction, informed and coordinated delivery room management, and planned univentricular surgical palliation.

摘要

多中心合作研究显著增进了我们对胎儿埃布斯坦畸形的理解,明确了不良结局的风险因素以及产后管理的预测指标。这些数据被纳入产前护理和治疗策略中,并为家庭咨询和分娩计划提供依据,以优化护理。本报告详细介绍了将多中心研究结果转化为针对患有埃布斯坦畸形、室上性心动过速和环状分流的胎儿的多学科产前护理,包括经胎盘治疗以控制心律失常并实现动脉导管收缩、明智且协调的产房管理,以及计划性单心室手术姑息治疗。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e382/11122070/1e5c0e06dfb8/jcdd-11-00147-g005.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e382/11122070/21fa15ce39b1/jcdd-11-00147-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e382/11122070/8c165f56f305/jcdd-11-00147-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e382/11122070/59b67d8b374c/jcdd-11-00147-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e382/11122070/71186aeb32dd/jcdd-11-00147-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e382/11122070/1e5c0e06dfb8/jcdd-11-00147-g005.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e382/11122070/21fa15ce39b1/jcdd-11-00147-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e382/11122070/8c165f56f305/jcdd-11-00147-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e382/11122070/59b67d8b374c/jcdd-11-00147-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e382/11122070/71186aeb32dd/jcdd-11-00147-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e382/11122070/1e5c0e06dfb8/jcdd-11-00147-g005.jpg

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J Cardiovasc Dev Dis. 2024 Mar 31;11(4):108. doi: 10.3390/jcdd11040108.
2
Pharmacological Management of Cardiac Arrhythmias in the Fetal and Neonatal Periods: A Scientific Statement From the American Heart Association: Endorsed by the Pediatric & Congenital Electrophysiology Society (PACES).胎儿和新生儿期心律失常的药理学处理:美国心脏协会的科学声明:得到儿科和先天性电生理学学会(PACES)的认可。
Circulation. 2024 Mar 5;149(10):e937-e952. doi: 10.1161/CIR.0000000000001206. Epub 2024 Feb 5.
3
Transplacental non-steroidal anti-inflammatory drugs versus expectant management in fetal Ebstein anomaly with circular shunt: Systematic review and meta-analysis.
经胎盘使用非甾体类抗炎药与期待治疗对伴有环形分流的胎儿埃布斯坦畸形:系统评价和荟萃分析。
Prenat Diagn. 2024 Jun;44(6-7):773-782. doi: 10.1002/pd.6446. Epub 2023 Oct 30.
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Guidelines and Recommendations for Performance of the Fetal Echocardiogram: An Update from the American Society of Echocardiography.胎儿超声心动图检查指南与建议:美国超声心动图学会的更新内容
J Am Soc Echocardiogr. 2023 Jul;36(7):679-723. doi: 10.1016/j.echo.2023.04.014. Epub 2023 May 24.
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Fetal Arrhythmia Diagnosis and Pharmacologic Management.胎儿心律失常的诊断与药物治疗。
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Evidence-Based Guidelines for Acute Stabilization and Management of Neonates with Persistent Pulmonary Hypertension of the Newborn.证据为基础的指南:新生儿持续肺动脉高压的急性稳定化和管理。
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