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大动脉炎中的罕见多部位动脉瘤:一个独特且具有挑战性的病例。

Exceptional multisite aneurysms in Takayasu arteritis: A unique and challenging case.

作者信息

Echeverria-Ortegon Ermilo, Millet-Herrera Jose Luis, Méndez-Molina Ricardo, Casillas Javier

机构信息

School of Medicine, Universidad Marista de Mérida, Periférico Norte Tablaje Catastral 13941, Temozón Nte, 97300 Mérida, Yuc.

Department of Radiology, University of Miami Health System, Miller School of Medicine, 1320 S Dixie Hwy, Coral Gables, FL 33146, EE. UU, Miami, FL, USA.

出版信息

Radiol Case Rep. 2024 May 22;19(8):3345-3348. doi: 10.1016/j.radcr.2024.04.056. eCollection 2024 Aug.

DOI:10.1016/j.radcr.2024.04.056
PMID:38832341
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC11145216/
Abstract

This case describes a rare and complex presentation of Takayasu arteritis, a large vessel vasculitis primarily affecting young females. Unlike typical Takayasu arteritis cases characterized by arterial stenosis, this 34-year-old male presented with an unusually high number of aneurysms affecting the aorta, subclavian arteries, and other segments. This unique abundance of aneurysms complicates diagnosis and management. This disease typically manifests as arterial stenosis, with aneurysms occurring in a minority of cases. The most common site for aneurysms is the ascending aorta, making multifocal aneurysms, as seen in this case, exceptionally rare. Managing multiple aneurysms in Takayasu arteritis is complex, necessitating careful consideration of factors like aneurysm size, morphology, and risk of complications. This case underscores the unique challenges posed by multifocal aneurysms in this condition, highlighting the need for a comprehensive approach to treatment.

摘要

该病例描述了一例罕见且复杂的大动脉炎表现,大动脉炎是一种主要影响年轻女性的大血管血管炎。与以动脉狭窄为特征的典型大动脉炎病例不同,这位34岁男性患者出现了数量异常多的动脉瘤,累及主动脉、锁骨下动脉和其他节段。这种独特的大量动脉瘤情况使诊断和治疗复杂化。该疾病通常表现为动脉狭窄,少数情况下会出现动脉瘤。动脉瘤最常见的部位是升主动脉,如此病例中所见的多灶性动脉瘤极为罕见。大动脉炎中多个动脉瘤的治疗很复杂,需要仔细考虑动脉瘤大小、形态和并发症风险等因素。该病例凸显了这种情况下多灶性动脉瘤带来的独特挑战,强调了需要采取综合治疗方法。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2e75/11145216/6169a865d895/gr2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2e75/11145216/eb9383360f47/gr1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2e75/11145216/6169a865d895/gr2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2e75/11145216/eb9383360f47/gr1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2e75/11145216/6169a865d895/gr2.jpg

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本文引用的文献

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Takayasu arteritis - epidemiology, pathogenesis, diagnosis and treatment.高安动脉炎——流行病学、发病机制、诊断与治疗
J Appl Biomed. 2019 Mar;17(1):20. doi: 10.32725/jab.2018.005. Epub 2019 Jan 9.
2
Multiple Aneurysms of the Subclavian-Axillary, Abdominal Aortoiliac, Lower Extremity, and Coronary Arteries in A Pediatric Patient of Takayasu Arteritis.一名大动脉炎儿科患者的锁骨下-腋动脉、腹主动脉-髂动脉、下肢及冠状动脉多发动脉瘤
Ann Vasc Surg. 2022 Apr;81:387.e1-387.e8. doi: 10.1016/j.avsg.2021.08.012. Epub 2021 Oct 15.
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Takayasu's Arteritis with a Thrombosed Aneurysm on the Common Carotid Artery Causing Ischemic Stroke.
颈总动脉血栓性动脉瘤导致的 Takayasu 动脉炎引起的缺血性脑卒中。
Intern Med. 2022 Feb 1;61(3):425-428. doi: 10.2169/internalmedicine.7735-21. Epub 2021 Jul 30.
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Successful Treatment of Giant Ascending Aortic Aneurysm with Takayasu Arteritis.
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Takayasu Arteritis with Dyslipidemia Increases Risk of Aneurysm.Takayasu 动脉炎伴血脂异常增加动脉瘤风险。
Sci Rep. 2019 Oct 1;9(1):14083. doi: 10.1038/s41598-019-50527-z.
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Takayasu arteritis: an update.高安动脉炎:最新进展
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Takayasu arteritis: advanced understanding is leading to new horizons.Takayasu 动脉炎:深入了解带来新视野。
Rheumatology (Oxford). 2019 Feb 1;58(2):206-219. doi: 10.1093/rheumatology/key040.
8
Aortic Aneurysm in Takayasu Arteritis.
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9
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