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大动脉炎的不寻常表现:诊断难题

Unusual manifestations of Takayasu arteritis: A diagnostic challenge.

作者信息

Al-Kinani Tahseen Ali, Al-Yacopy Ali Akeel, Alhatemi Ahmed Qasim Mohammed, Hashim Hashim Talib, Abdulhussain Rand, Hashim Ali Talib

机构信息

Coronary Care Unit Al Nasiriyah Heart Hospital Thi Qar Iraq.

Internal Medicine Al Nasiriyah Teaching Hospital Thi Qar Iraq.

出版信息

Clin Case Rep. 2024 Jun 3;12(6):e9051. doi: 10.1002/ccr3.9051. eCollection 2024 Jun.

DOI:10.1002/ccr3.9051
PMID:38836110
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC11147744/
Abstract

KEY CLINICAL MESSAGE

Timely recognition of atypical Takayasu arteritis is crucial. Unusual presentations, such as pericardial effusion, can complicate diagnosis. CT angiogram aids in precise diagnosis, guiding targeted immunosuppressive therapy. Multidisciplinary collaboration is vital for comprehensive management, improving patient outcomes in this challenging condition.

ABSTRACT

This case study highlights the diagnostic challenges posed by atypical presentations of Takayasu arteritis (TA), focusing on a 42-year-old male presenting with pericardial effusion. Despite inconclusive initial investigations, a CT angiogram revealed large vessel vasculitis, confirming TA. Management with immunosuppressive therapy led to clinical improvement. This case emphasize the importance of recognizing unusual manifestations of TA for timely diagnosis and appropriate treatment, emphasizing the role of multidisciplinary collaboration in optimizing patient outcomes.

摘要

关键临床信息

及时识别非典型大动脉炎至关重要。不寻常的表现,如心包积液,会使诊断复杂化。CT血管造影有助于精确诊断,指导针对性的免疫抑制治疗。多学科协作对于全面管理至关重要,可改善这种具有挑战性疾病的患者预后。

摘要

本病例研究突出了大动脉炎(TA)非典型表现所带来的诊断挑战,重点关注一名出现心包积液的42岁男性。尽管初始检查结果不明确,但CT血管造影显示大血管血管炎,确诊为TA。免疫抑制治疗使病情得到临床改善。本病例强调了识别TA不寻常表现对于及时诊断和恰当治疗的重要性,凸显了多学科协作在优化患者预后方面的作用。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4c15/11147744/4d22866f8945/CCR3-12-e9051-g006.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4c15/11147744/e5b753d08548/CCR3-12-e9051-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4c15/11147744/e9f37eb1d728/CCR3-12-e9051-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4c15/11147744/c8c408a6a816/CCR3-12-e9051-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4c15/11147744/8326fc820593/CCR3-12-e9051-g005.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4c15/11147744/4d22866f8945/CCR3-12-e9051-g006.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4c15/11147744/e5b753d08548/CCR3-12-e9051-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4c15/11147744/e9f37eb1d728/CCR3-12-e9051-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4c15/11147744/c8c408a6a816/CCR3-12-e9051-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4c15/11147744/8326fc820593/CCR3-12-e9051-g005.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4c15/11147744/4d22866f8945/CCR3-12-e9051-g006.jpg

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Takayasu arteritis: challenges in diagnosis and management.Takayasu 动脉炎:诊断和治疗中的挑战。
Heart. 2018 Apr;104(7):558-565. doi: 10.1136/heartjnl-2016-310848. Epub 2017 Nov 25.
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Clin Exp Rheumatol. 2017 Mar-Apr;35 Suppl 103(1):189-193. Epub 2017 Mar 27.
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Diagnosis and assessment of disease activity in takayasu arteritis: a childhood case illustrating the challenge.大动脉炎疾病活动的诊断与评估:一个说明挑战的儿童病例
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Diagnostic features, treatment, and outcomes of Takayasu arteritis in a US cohort of 126 patients.126 例美国患者中 Takayasu 动脉炎的诊断特征、治疗和转归。
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