Guelzim Yousra, Halfi Mohamed Ismail, Marrakchi Salma, Krioule Soumia, Tahri Salma, El Yousfi Mounia, El Hassouni Fatima, Maakoul Rachid, Allali Nazik, Chat Latifa, El Haddad Siham
Department of Radiology, Ibn Sina Paediatric Teaching Hospital, Mohammed V University, Rabat, Morocco.
Department of Obstetrics and Gynecology, Oncology and, High-Risk Pregnancies, Maternity Souissi Ibn Sina, University Mohammed V Rabat, Morocco.
Radiol Case Rep. 2024 Jun 1;19(8):3478-3482. doi: 10.1016/j.radcr.2024.05.003. eCollection 2024 Aug.
Conjoined twins occur in an estimated one in every 200,000 live births. The etiology remains largely speculative, with genetic and environmental factors being considered. The thoraco-omphalopagus type accounts for approximately 40% of cases, making it a focal point for clinical and radiological research. Radiological imaging plays a pivotal role in delineating anatomical details, offering insights into the feasibility of surgical interventions and informing parental counselling regarding prognosis and management options. We present a case of thoracoomphalogus conjoined twins diagnosed during the third trimester of pregnancy in a 19-year-old woman. The detailed radiological assessment using ultra-sound and MRI provided crucial information on organ sharing and vascular anatomy, which is critical for management strategies. This case underscores the critical role of prenatal imaging in detecting complex congenital anomalies, facilitating informed decision-making by healthcare providers and families.
联体双胎的发生率约为每20万例活产中有1例。其病因在很大程度上仍属推测,人们认为与遗传和环境因素有关。胸腹联体类型约占病例的40%,使其成为临床和放射学研究的重点。放射影像学在描绘解剖细节方面起着关键作用,有助于了解手术干预的可行性,并为父母提供有关预后和管理方案的咨询信息。我们报告一例19岁女性在妊娠晚期诊断出的胸腹联体双胎病例。使用超声和MRI进行的详细放射学评估提供了关于器官共享和血管解剖的关键信息,这对管理策略至关重要。该病例强调了产前影像学在检测复杂先天性畸形方面的关键作用,有助于医疗服务提供者和家庭做出明智的决策。