Di Liberto Ilenia Alessandra, Pilato Gerlando, Caramanno Giuseppe
Department of Interventional Cardiology, San Giovanni Di Dio Hospital, Agrigento, Italy.
ARYA Atheroscler. 2023 Jan;19(1):61-64. doi: 10.48305/arya.2022.11722.2343.
Ehlers-Danlos syndrome (EDS) is a hereditary collagen vascular disorder characterized by joint hypermobility, skin hyperextensibility, and tissue fragility. Vascular EDS (vEDS) is a subtype of EDS which is characterized by vascular fragility.
This is a case report of a young man with vEDS hospitalized for myocardial infarction. He was presented with a coronary dissection and developed aortic dissection, coronary rupture, and cardiac tamponade until death.
This case report highlights how patients with vEDS and acute coronary syndrome show a higher risk of vascular complications compared with other patients, and their admission to the institution with a cardiac surgery room could be helpful and safe for better management of the complications. Non-invasive methods could be useful to exclude other vascular diseases, before the emergency coronary intervention.
埃勒斯-当洛综合征（EDS）是一种遗传性胶原血管疾病，其特征为关节活动过度、皮肤过度伸展和组织脆弱。血管型埃勒斯-当洛综合征（vEDS）是EDS的一种亚型，其特征为血管脆弱。
本文报告一例因心肌梗死住院的年轻vEDS男性患者。他出现冠状动脉夹层，并发展为主动脉夹层、冠状动脉破裂和心脏压塞，最终死亡。
本病例报告强调，与其他患者相比，vEDS和急性冠状动脉综合征患者出现血管并发症的风险更高，将他们收治入设有心脏手术室的机构，有助于更安全地管理并发症。在进行紧急冠状动脉介入治疗之前，非侵入性方法可能有助于排除其他血管疾病。
