Jerkovic Gulin Sandra, Ilic Ivana, Ceovic Romana
Department of Dermatology and Venereology, Ryhov County Hospital, 551 85 Jonkoping, Sweden.
Department of Biomedical and Clinical Sciences, Faculty of Medicine and Health Sciences, Linkoping University, 581 85 Linkoping, Sweden.
Dermatopathology (Basel). 2024 Jun 14;11(2):161-176. doi: 10.3390/dermatopathology11020017.
Primary cutaneous lymphomas (PCLs), especially mycosis fungoides (MF), pose significant diagnostic and therapeutic challenges. This study aims to correlate initial histological features with the disease course and survival in MF patients. A retrospective-prospective cohort study was conducted on 83 patients diagnosed with early-stage MF at the Departments of Dermatovenerology and Pathology, UHC Zagreb, from January 2003 to December 2012. The analyzed histopathological parameters included lichenoid dermal lymphocyte infiltrate, Pautrier microabscesses, and lymphocyte atypia. Patients with more than 30 guardian lymphocytes per 100 keratinocytes exhibited worse overall and progression-free survival. Furthermore, those with over 50% atypical lymphocytes demonstrated a faster progression rate. A dense lichenoid dermal infiltrate and a high count of lymphocyte "keepers" significantly increased the mortality risk within five years of diagnosis. This study did not fully confirm the hypothesis regarding the prognostic value of large Pautrier microabscesses but highlighted the importance of dense lichenoid infiltrates. The study identified new potential histopathological prognostic factors in early-stage MF, suggesting the need for larger studies to confirm these findings. The identification of such predictors could enhance the prognostic stratification and guide more tailored therapeutic approaches for MF patients.
原发性皮肤淋巴瘤(PCLs),尤其是蕈样肉芽肿(MF),带来了重大的诊断和治疗挑战。本研究旨在将MF患者的初始组织学特征与疾病进程及生存情况相关联。2003年1月至2012年12月期间,在萨格勒布大学医院中心皮肤科和病理科对83例诊断为早期MF的患者进行了一项回顾性-前瞻性队列研究。分析的组织病理学参数包括苔藓样真皮淋巴细胞浸润、Pautrier微脓肿和淋巴细胞异型性。每100个角质形成细胞中监护淋巴细胞超过30个的患者总体生存和无进展生存情况较差。此外,异型淋巴细胞超过50%的患者疾病进展速度更快。致密的苔藓样真皮浸润和高计数的淋巴细胞“守护者”显著增加了诊断后五年内的死亡风险。本研究未完全证实关于大Pautrier微脓肿预后价值的假设,但强调了致密苔藓样浸润的重要性。该研究确定了早期MF中新的潜在组织病理学预后因素,表明需要开展更大规模的研究来证实这些发现。识别此类预测指标可加强预后分层,并为MF患者指导更具针对性的治疗方法。