Wu Patricia, Becker Francisco Barros, Ogelman Roberto, Camci Esra D, Linbo Tor H, Simon Julian A, Rubel Edwin W, Raible David W
Virginia Merrill Bloedel Hearing Research Center, University of Washington, Seattle, WA 98195, United States.
Department of Biological Structure, University of Washington, Seattle, WA 98195, United States.
bioRxiv. 2024 Jul 12:2024.05.30.596537. doi: 10.1101/2024.05.30.596537.
Mechanosensory hair cells of the inner ears and lateral line of vertebrates display heightened vulnerability to environmental insult, with damage resulting in hearing and balance disorders. An important example is hair cell loss due to exposure to toxic agents including therapeutic drugs such as the aminoglycoside antibiotics such as neomycin and gentamicin and antineoplastic agents. We describe two distinct cellular pathways for aminoglycoside-induced hair cell death in zebrafish lateral line hair cells. Neomycin exposure results in death from acute exposure with most cells dying within 1 hour of exposure. By contrast, exposure to gentamicin results primarily in delayed hair cell death, taking up to 24 hours for maximal effect. Washout experiments demonstrate that delayed death does not require continuous exposure, demonstrating two mechanisms where downstream responses differ in their timing. Acute damage is associated with mitochondrial calcium fluxes and can be alleviated by the mitochondrially-targeted antioxidant mitoTEMPO, while delayed death is independent of these factors. Conversely delayed death is associated with lysosomal accumulation and is reduced by altering endolysosomal function, while acute death is not sensitive to lysosomal manipulations. These experiments reveal the complexity of responses of hair cells to closely related compounds, suggesting that intervention focusing on early events rather than specific death pathways may be a successful therapeutic strategy.
脊椎动物内耳和侧线的机械感觉毛细胞对环境损伤表现出高度易感性,损伤会导致听力和平衡障碍。一个重要的例子是由于接触包括治疗药物如新霉素和庆大霉素等氨基糖苷类抗生素以及抗肿瘤药物在内的有毒物质而导致的毛细胞损失。我们描述了斑马鱼侧线毛细胞中氨基糖苷类药物诱导毛细胞死亡的两种不同细胞途径。新霉素暴露导致急性暴露死亡,大多数细胞在暴露后1小时内死亡。相比之下,暴露于庆大霉素主要导致延迟性毛细胞死亡,最大效应需要长达24小时。洗脱实验表明,延迟死亡不需要持续暴露,这证明了两种下游反应在时间上不同的机制。急性损伤与线粒体钙通量有关,并且可以通过线粒体靶向抗氧化剂mitoTEMPO来缓解,而延迟死亡与这些因素无关。相反,延迟死亡与溶酶体积累有关,并且通过改变内溶酶体功能而减少,而急性死亡对溶酶体操作不敏感。这些实验揭示了毛细胞对密切相关化合物反应的复杂性,表明关注早期事件而非特定死亡途径的干预可能是一种成功的治疗策略。