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散发性克雅氏病中以构音障碍为首发症状并伴有快速进展性影像学特征:一例报告

Dysarthria as a Presenting Symptom With Rapidly Progressive Imaging Features in Sporadic Creutzfeldt-Jakob Disease: A Case Report.

作者信息

Pan Tengwei, Wang Shanshan

机构信息

Neurology, Taizhou Hospital of Zhejiang Province Affiliated to Wenzhou Medical University, Taizhou, CHN.

出版信息

Cureus. 2024 Jun 19;16(6):e62687. doi: 10.7759/cureus.62687. eCollection 2024 Jun.

Abstract

Sporadic Creutzfeldt-Jakob disease (sCJD) is a rare and fatal neurodegenerative disorder belonging to a group of diseases known as prion disease. Characterized by the formation of abnormal prion proteins in the brain, these conditions lead to tissue damage and vacuolation, giving the brain a sponge-like appearance. sCJD represents the most prevalent form of CJD, accounting for roughly 85% of all CJD cases. We report a case with unusual clinical manifestations. The patient experienced progressive neurological symptoms and MRI progression.

摘要

散发性克雅氏病(sCJD)是一种罕见的致命性神经退行性疾病,属于一组被称为朊病毒病的疾病。其特征是大脑中形成异常的朊病毒蛋白,这些情况会导致组织损伤和空泡化,使大脑呈现出海绵状外观。sCJD是克雅氏病最常见的形式,约占所有克雅氏病病例的85%。我们报告了一例具有不寻常临床表现的病例。该患者出现进行性神经症状和MRI进展。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8c3a/11259518/f0c78c07e9a5/cureus-0016-00000062687-i01.jpg

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