Department of Ophthalmology, Faculdade de Medicina, Universidade de São Paulo, São Paulo, SP, Brazil.
Department of Radiology, Hospital de Clínicas, Universidade Federal do Paraná, Curitiba, PR, Brazil.
Arq Bras Oftalmol. 2024 Aug 5;88(1):e20220195. doi: 10.5935/0004-2749.2022-0195. eCollection 2024.
A young woman presented at our clinic with sudden visual loss in the right eye, recurrent vertigo, and right-sided tinnitus. We performed a complete ophthalmological evaluation. This revealed effects of the condition on the small arterioles of the peripheral retina. Susac syndrome is characterized by the clinical triad of retinal arteriolar occlusions, cochleovestibular manifestations, and encephalopathy (which can be identified by neuroimaging abnormalities). Early diagnosis and immunosuppressive therapy improved the patient's visual acuity and the remission of her other symptoms. Hemi-central retinal artery occlusion is an atypical neuro-ophthalmological finding in this disease. However, its identification as a sign of Susac syndrome may facilitate timely diagnosis and accurate treatment.
一位年轻女性因右眼突发性视力丧失、反复发作性眩晕和右侧耳鸣到我院就诊。我们进行了全面的眼科评估。结果显示，该患者的眼底小动脉受到了影响。Susac 综合征的特征是视网膜小动脉阻塞、耳蜗前庭表现和脑病三联征（可通过神经影像学异常识别）。早期诊断和免疫抑制治疗改善了患者的视力和其他症状的缓解。半侧中央视网膜动脉阻塞是该疾病中一种非典型的神经眼科表现。然而，将其识别为 Susac 综合征的一个征象可能有助于及时诊断和准确治疗。
