Gaffoor Nidha, Mysorekar Vijaya V, Gunadal Shankar, Divyashree B N, Sandeepa Supriya, Murali Nirupama
Department of Pathology, Dr. Chandramma Dayananda Sagar Institute of Medical Education and Research, Dayananda Sagar University, Ramanagara, Karnataka, India.
Department of Urology, Dr. Chandramma Dayananda Sagar Institute of Medical Education and Research, Dayananda Sagar University, Ramanagara, Karnataka, India.
Indian J Nephrol. 2024 May-Jun;34(3):271-273. doi: 10.4103/ijn.ijn_397_23. Epub 2023 Nov 6.
Renal angiomyolipoma (AML) is a benign mesenchymal tumor composed of fat, smooth muscle, and blood vessels. It represents 1-3% of solid renal tumors. Despite the benign nature of this tumor, it can be aggressive with locoregional extension. We describe a case of a 60-year-old female who presented with left flank pain and unstable blood pressure. A CT scan showed a renal mass with hemorrhagic densities. Peroperatively, bleeding from the renal mass was revealed, and the patient underwent radical nephrectomy. A myriad of symptoms such as acute flank pain, flank mass, and bleeding led to the diagnosis of Wunderlich syndrome, which is usually seen secondary to AML and renal cell carcinoma. Histopathologic examination helped in arriving at the diagnosis of renal AML with secondary changes, ruling out malignancy. Early diagnosis and immediate intervention saved her life and reduced morbidity. This case report helps in sensitizing clinicians and thus facilitates the detection of similar cases at the earliest.
肾血管平滑肌脂肪瘤（AML）是一种由脂肪、平滑肌和血管组成的良性间叶性肿瘤。它占实性肾肿瘤的1%-3%。尽管该肿瘤具有良性本质，但它可能具有侵袭性并发生局部区域扩展。我们描述了一例60岁女性患者，她出现左侧腰痛和血压不稳定。CT扫描显示一个具有出血密度的肾肿块。术中发现肾肿块出血，患者接受了根治性肾切除术。诸如急性腰痛、腰部肿块和出血等众多症状导致了温德利希综合征的诊断，该综合征通常继发于AML和肾细胞癌。组织病理学检查有助于确诊为伴有继发性改变的肾AML，排除恶性肿瘤。早期诊断和立即干预挽救了她的生命并降低了发病率。本病例报告有助于提高临床医生的认识，从而便于尽早发现类似病例。
