Al Umairi Rashid, Al Shamsi Ruqaiya, Kamona Atheel, Al Lawati Fatma, Baqi Sadiq Abdul, Kurian Geroge, Al Kalbani Jokha
Radiology Department, Royal Hospital, Muscat, Oman.
Histopathology Department, Royal Hospital, Muscat, Oman.
Oman Med J. 2020 Sep 30;35(5):e178. doi: 10.5001/omj.2020.. eCollection 2020 Sep.
Epithelioid angiomyolipoma (EAML) is an uncommon renal neoplasm with malignant potential. It is classified under the group of perivascular epithelioid cell tumors and can be sporadic or as part of the tuberous sclerosis complex. On imaging, unlike classical AML that contains fat, EAML has a very low percentage of fat which can mimic the imaging findings of renal cell carcinoma. We reported a 31-year-old female who had a history of renal failure and bilateral renal masses. Magnetic resonance imaging of the abdomen revealed bilateral large renal masses replacing renal parenchyma with features suggestive of bilateral renal AML. The patient underwent left nephrectomy, and histopathology examination findings were consistent with the diagnosis of EAML.
上皮样血管平滑肌脂肪瘤(EAML)是一种具有恶性潜能的罕见肾肿瘤。它被归类于血管周上皮样细胞瘤组,可散发或作为结节性硬化症复合体的一部分。在影像学上,与含有脂肪的经典血管平滑肌脂肪瘤不同,EAML的脂肪含量极低,可模拟肾细胞癌的影像学表现。我们报告了一名31岁女性,有肾衰竭和双侧肾肿块病史。腹部磁共振成像显示双侧大的肾肿块取代肾实质,具有双侧肾血管平滑肌脂肪瘤的特征。患者接受了左肾切除术,组织病理学检查结果与EAML诊断一致。