Al-Juboori Ahmed A, Badran Saif A, Shahadha Ali A, Alsamok Ali S, Ismail Mustafa
Department of Neurosurgery, Dr. Sa'ad AL-Witri Hospital for Neurosciences, Baghdad, IRQ.
Department of Surgery, Ibn Sina University of Medical and Pharmaceutical Sciences, Baghdad, IRQ.
Cureus. 2024 Jul 14;16(7):e64525. doi: 10.7759/cureus.64525. eCollection 2024 Jul.
Pituitary apoplexy is a rare but potentially life-threatening condition of sudden hemorrhage or infarction within the pituitary gland that results in symptoms of acute onset such as severe headache, visual impairment, and hormonal deficiencies. Though more common in adults, the same criteria for diagnostic and management dilemmas apply to pediatric cases. We present the case of a nine-year-old boy presenting with acute-onset severe headache and significant visual deterioration suggestive of pituitary apoplexy. An emergency MRI was performed, which showed a hemorrhagic sellar and suprasellar mass compressing the optic chiasm. Given the severe visual symptoms in this case, emergency surgical intervention was indicated. Decompression and gross total resection of the tumor were successfully attained using the endoscopic transnasal transsphenoidal approach by a multidisciplinary team. After the surgery, there was a significant improvement in the visual field, especially regarding the right eye's nasal hemifield, and the motor strength and consciousness remained stable. This case underscores the importance of early diagnosis and expedited surgical management in pediatric pituitary apoplexy. The transnasal transsphenoidal approach is practical for maximal decompression of the optic apparatus and reduces the risk of long-term visual deficits. In addition, it points out the need for coordinated, multidisciplinary treatment with the participation of neurosurgeons, endocrinologists, and pediatricians both for immediate and long-term consequences, including potential hormonal deficiencies. The report emphasizes the need for vigilance and prompt intervention in pediatric presentations, unlike the index case, for better outcomes and to avoid permanent morbidity.
垂体卒中是一种罕见但可能危及生命的疾病,指垂体突然出血或梗死,导致急性发作的症状,如严重头痛、视力障碍和激素缺乏。虽然在成人中更常见,但诊断和处理难题的相同标准也适用于儿科病例。我们报告一例9岁男孩,出现急性发作的严重头痛和明显视力恶化,提示垂体卒中。进行了急诊MRI检查,结果显示鞍内和鞍上有出血性肿块压迫视交叉。鉴于该病例严重的视觉症状,需要进行急诊手术干预。一个多学科团队通过内镜经鼻蝶窦入路成功实现了肿瘤减压和全切。手术后,视野有显著改善,尤其是右眼鼻侧半视野,肌力和意识保持稳定。该病例强调了小儿垂体卒中早期诊断和快速手术治疗的重要性。经鼻蝶窦入路对于视器的最大程度减压是可行的,并降低了长期视力缺陷的风险。此外表明,对于包括潜在激素缺乏在内的近期和远期后果,需要神经外科医生、内分泌科医生和儿科医生参与的协调多学科治疗。该报告强调,与索引病例不同,对于儿科病例需要保持警惕并及时干预,以获得更好效果并避免永久性发病。