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原发于心房间隔的滑膜肉瘤并肺梗死 1 例报告

Primary cardiac synovial sarcoma originating from the atrial septum and associated pulmonary infarction: a case report.

机构信息

Department of Oncology, Chengdu First People's Hospital, Chengdu, China.

Department of Cardiovascular Surgery, Chengdu First People's Hospital, Chengdu, China.

出版信息

J Cancer Res Clin Oncol. 2024 Aug 20;150(8):392. doi: 10.1007/s00432-024-05852-w.

DOI:10.1007/s00432-024-05852-w
PMID:39162837
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC11335867/
Abstract

BACKGROUND

Primary cardiac synovial sarcoma is a rare condition with limited treatment options for advanced stages. Surgery and chemotherapy are currently the mainstay treatments; however, survival rates remain low.

CASE PRESENTATION

A 64-year-old woman presenting with symptoms of chest tightness and shortness of breath was found to have an obstructive right atrial mass, along with pulmonary infarction and metastasis. She was ultimately diagnosed with advanced primary cardiac synovial sarcoma. Following surgery, the patient's symptoms improved, and she underwent chemotherapy and anti-angiogenic therapy, but unfortunately, her survival time was only 8 months.

CONCLUSION

This case report aims to enhance clinicians' understanding of the diagnosis and treatment of primary cardiac synovial sarcoma. Enhancing both survival outcomes and quality of life in individuals with primary cardiac synovial sarcoma continues to present a significant challenge.

摘要

背景

原发性心脏滑膜肉瘤是一种罕见疾病,晚期治疗选择有限。手术和化疗是目前的主要治疗方法;然而,生存率仍然很低。

病例介绍

一位 64 岁女性出现胸闷和呼吸急促的症状,被发现有一个阻塞性右心房肿块,同时伴有肺梗死和转移。她最终被诊断为晚期原发性心脏滑膜肉瘤。手术后,患者症状改善,接受了化疗和抗血管生成治疗,但不幸的是,她的生存时间仅为 8 个月。

结论

本病例报告旨在提高临床医生对原发性心脏滑膜肉瘤的诊断和治疗的认识。提高原发性心脏滑膜肉瘤患者的生存率和生活质量仍然是一个重大挑战。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4264/11335867/f51ff7ebcf3f/432_2024_5852_Fig4_HTML.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4264/11335867/af8935f2ed26/432_2024_5852_Fig1_HTML.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4264/11335867/3d509cee8a43/432_2024_5852_Fig2_HTML.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4264/11335867/a01b3795861c/432_2024_5852_Fig3_HTML.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4264/11335867/f51ff7ebcf3f/432_2024_5852_Fig4_HTML.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4264/11335867/af8935f2ed26/432_2024_5852_Fig1_HTML.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4264/11335867/3d509cee8a43/432_2024_5852_Fig2_HTML.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4264/11335867/a01b3795861c/432_2024_5852_Fig3_HTML.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4264/11335867/f51ff7ebcf3f/432_2024_5852_Fig4_HTML.jpg

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