Hatty S, Mufti G J, Hamblin T J
Acta Haematol. 1985;73(1):37-9. doi: 10.1159/000206270.
Angio-immunoblastic lymphadenopathy is a systemic disease of unknown aetiology. It carries a high mortality mainly from infection which results both from the intrinsic immunodeficiency and its exacerbation by treatment with steroids and or cytotoxics. We report a case of angio-immunoblastic lymphadenopathy with the unusual feature of hypogammaglobulinaemia who died of miliary tuberculosis. We suggest that all patients with angio-immunoblastic lymphadenopathy who have inactive tuberculous foci should be given antituberculous prophylaxis.
血管免疫母细胞性淋巴结病是一种病因不明的全身性疾病。它具有较高的死亡率,主要死于感染,这既源于内在的免疫缺陷,也源于类固醇和/或细胞毒性药物治疗导致的免疫缺陷加剧。我们报告一例血管免疫母细胞性淋巴结病患者,其具有低丙种球蛋白血症这一不寻常特征,死于粟粒性肺结核。我们建议,所有患有血管免疫母细胞性淋巴结病且有非活动性结核病灶的患者都应接受抗结核预防治疗。