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镰状细胞贫血患者节段性睾丸梗死的保守治疗:一例报告

Conservative management of segmental testicular infarction in a patient with sickle cell anemia: A case report.

作者信息

Wu Sarah Y, Gibbs Evan Mackenize, Klose Charles, Qosja Neda, Zganjar Andrew, Baird Bryce A

机构信息

Mayo Clinic Alix School of Medicine, Scottsdale, AZ, USA.

Mayo Clinic Florida, Department of Urology, Jacksonville, FL, USA.

出版信息

Urol Case Rep. 2024 Jun 21;56:102775. doi: 10.1016/j.eucr.2024.102775. eCollection 2024 Sep.

DOI:10.1016/j.eucr.2024.102775
PMID:39239098
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC11375290/
Abstract

Vaso-occlusive crisis is a sequela of sickle cell disease that can lead to severe pain and infarction at the location of occlusion. In men, genitourinary complications include priapism, hematuria, and very rarely, testicular infarction. Few cases have been previously reported in the literature, but in all of those cases, partial or complete orchiectomy was performed. We report the first known case of segmental testicular infarct secondary to sickle cell disease treated with medical management without need for surgical intervention.

摘要

血管闭塞性危机是镰状细胞病的一种后遗症,可导致闭塞部位出现严重疼痛和梗死。在男性中,泌尿生殖系统并发症包括阴茎异常勃起、血尿,以及极为罕见的睾丸梗死。此前文献中鲜有病例报道,但所有这些病例均进行了部分或全睾丸切除术。我们报告了首例已知的镰状细胞病继发节段性睾丸梗死病例,该病例通过药物治疗得以治愈,无需手术干预。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6e2a/11375290/45c4b0fe115b/gr2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6e2a/11375290/ef5a21a18101/gr1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6e2a/11375290/45c4b0fe115b/gr2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6e2a/11375290/ef5a21a18101/gr1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6e2a/11375290/45c4b0fe115b/gr2.jpg

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引用本文的文献

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Bilateral segmental testicular infarction secondary to iron deficiency anemia: a case report.缺铁性贫血继发双侧节段性睾丸梗死:一例报告
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本文引用的文献

1
The vaso-occlusive pain crisis in sickle cell disease: Definition, pathophysiology, and management.镰状细胞病的血管阻塞性疼痛危象:定义、病理生理学和治疗。
Eur J Haematol. 2020 Sep;105(3):237-246. doi: 10.1111/ejh.13430. Epub 2020 May 19.
2
Testicular infarction in a patient with sickle cell anemia: A case report.镰状细胞贫血患者的睾丸梗死:一例报告。
Int J Health Sci (Qassim). 2018 Sep-Oct;12(5):100-102.
3
Reproductive endocrine issues in men with sickle cell anemia.镰状细胞贫血男性患者的生殖内分泌问题。
Andrology. 2017 Jul;5(4):679-690. doi: 10.1111/andr.12370. Epub 2017 Jun 29.
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Sickle cell disease.镰状细胞病。
Lancet. 2017 Jul 15;390(10091):311-323. doi: 10.1016/S0140-6736(17)30193-9. Epub 2017 Feb 1.
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Acute segmental testicular infarction.急性节段性睾丸梗死
Int J Urol. 2006 May;13(5):651-2. doi: 10.1111/j.1442-2042.2006.01367.x.
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Repeated testicular infarction in a patient with sickle cell disease: a possible mechanism for testicular failure.镰状细胞病患者反复发生睾丸梗死:睾丸功能衰竭的一种可能机制。
Urology. 2003 Sep;62(3):551. doi: 10.1016/s0090-4295(03)00482-5.
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Genitourinary complications of sickle cell disease.镰状细胞病的泌尿生殖系统并发症
J Urol. 2001 Sep;166(3):803-11.
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Segmental testicular infarction due to sickle cell disease.镰状细胞病所致节段性睾丸梗死
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Pathogenesis and treatment of sickle cell disease.镰状细胞病的发病机制与治疗
N Engl J Med. 1997 Sep 11;337(11):762-9. doi: 10.1056/NEJM199709113371107.