Aljalahma Noora, Alkoheji Heba, Saunders Helen, Tareif Habib
Surgery, Military Hospital, Royal Medical Services, Riffa, BHR.
Internal Medicine, Military Hospital, Royal Medical Services, Riffa, BHR.
Cureus. 2024 Aug 6;16(8):e66340. doi: 10.7759/cureus.66340. eCollection 2024 Aug.
Ebstein anomaly is a congenital heart disease that is considered rare and mostly found in pediatrics population. Symptoms in adults vary depending on the degree of the valve displacement and include difficulty breathing, palpitations, stroke, or even fatigue. However, if it occurs in the elderly, they end up with a good prognosis. A novel calcium sensitizer "levosimendan" has been used perioperatively in heart valve replacement to improve the long-term prognosis of patients. The use of the drug has been shown to reduce postoperative mortality in patients with reduction in ejection fraction. We present the case of a 62-year-old female, a known case of hypothyroidism, bronchial asthma, gastroesophageal reflux disease, and recent diagnosis of Ebstein anomaly, who underwent tricuspid valve repair and atrial septal defect repair on being symptomatic, in addition to the successful use of a novel positive inotropic drug with decrease in the intensive care unit stay.
埃布斯坦畸形是一种先天性心脏病，较为罕见，多见于儿科人群。成人的症状因瓣膜移位程度而异，包括呼吸困难、心悸、中风，甚至疲劳。然而，如果发生在老年人身上，其预后良好。一种新型钙敏化剂“左西孟旦”已在心脏瓣膜置换术中围手术期使用，以改善患者的长期预后。该药物的使用已被证明可降低射血分数降低患者的术后死亡率。我们报告一例62岁女性病例，该患者已知患有甲状腺功能减退、支气管哮喘、胃食管反流病，最近诊断为埃布斯坦畸形，因出现症状接受了三尖瓣修复和房间隔缺损修复，此外还成功使用了一种新型正性肌力药物，缩短了重症监护病房的住院时间。
