Faraj Chaymae, Mahdi Youssef, Essetti Sara, Chait Fatima, Essaber Hatim, El Bakkari Asaad, Omor Youssef, Latib Rachida, Amalik Sanae, El Khannoussi Basma
Radiology department, National Institute of Oncology, Faculty of Medicine and Pharmacy, Mohammed V University, Rabat, Morocco.
Pathology department, National Institute of Oncology, Faculty of Medicine and Pharmacy, Mohammed V University, Rabat, Morocco.
Radiol Case Rep. 2024 Aug 17;19(11):4950-4954. doi: 10.1016/j.radcr.2024.07.107. eCollection 2024 Nov.
Primary hepatic leiomyosarcoma (PHL) is a rare malignant tumor, which originates from smooth muscles. The imaging features are nonspecific and the diagnosis is often delayed until the tumor reaches a large size, which leads often to a dismal prognosis. We report a case of a 46-year-old male patient who was complaining about abdominal pain for 2 months. The imaging revealed the presence of a large mass in the liver with adrenal and liver metastasis. Diagnosis of PHL was confirmed by histopathological and immunohistochemical examinations. In this case report, we review the epidemiological, clinical, and paraclinical aspects of the disease, as well as the treatment modalities.
原发性肝平滑肌肉瘤(PHL)是一种罕见的恶性肿瘤,起源于平滑肌。其影像学特征不具有特异性,诊断往往延迟,直到肿瘤长得很大,这常常导致预后不佳。我们报告一例46岁男性患者,他主诉腹痛2个月。影像学检查显示肝脏有一个大肿块,并伴有肾上腺和肝脏转移。通过组织病理学和免疫组织化学检查确诊为PHL。在本病例报告中,我们回顾了该疾病的流行病学、临床和辅助检查方面,以及治疗方式。