Jeong Tae Yeob, Kim You Sun, Park Kyung Jun, Lee Jong Sung, Huh Jin Gook, Ryu Soo Hyung, Lee Jung Hwan, Moon Jeong Seop
Department of Internal Medicine, Seoul Paik Hospital, Inje University College of Medicine, Seoul, Korea.
Korean J Gastroenterol. 2008 Mar;51(3):194-8.
Leiomyosarcoma is a rare tumor of the liver. It usually arises from many other organs including uterus, gastrointestinal tract, retroperitoneum, and soft tissues. Primary hepatic leiomyosarcoma progresses very slowly and is not associated with chronic liver disease. When the tumor is detected early enough to be treated by operation, the prognosis is favorable. While several cases of primary hepatic leiomyosarcoma have been reported in Korea, there was no case associated with acute bleeding. We report a 80-year old male patient with huge primary hepatic leiomyosarcoma, who presented with acute bleeding and IVC obstruction. The patient was treated by embolization and IVC stenting.
平滑肌肉瘤是一种罕见的肝脏肿瘤。它通常起源于包括子宫、胃肠道、腹膜后和软组织在内的许多其他器官。原发性肝平滑肌肉瘤进展非常缓慢,与慢性肝病无关。当肿瘤被早期发现并能够通过手术治疗时,预后良好。虽然韩国已经报道了几例原发性肝平滑肌肉瘤病例,但没有与急性出血相关的病例。我们报告了一名80岁男性患者,患有巨大的原发性肝平滑肌肉瘤,表现为急性出血和下腔静脉阻塞。该患者接受了栓塞和下腔静脉支架置入治疗。