Anesthesia Department, Fatouma Bourguiba Hospital, Monastir, Tunisia.
Neurosurgery Department, Fatouma Bourguiba Hospital, Monastir, Tunisia.
Pan Afr Med J. 2024 Apr 30;47:220. doi: 10.11604/pamj.2024.47.220.39924. eCollection 2024.
Pleomorphic xanthoastrocytoma (PXA) is a rare low-grade glial neoplasm of the central nervous system accounting for less than 1% of all astrocytomas. Similar to other gliomas, it can rarely arise from glial nests in the meninges, manifesting as an extra-axial mass mimicking a meningioma. Extra axial PXA is an extremely rare entity. Therefore, there are no standardized guidelines. In this article, we report the fourth case, so far, of a solitary primary extra-axial PXA mimicking a meningioma in a 23-year-old woman who presented with temporal seizures and features of raised intracranial pressure. Through this case, we tried to discuss all treatment options.
多形性黄色星形细胞瘤(PXA)是一种罕见的中枢神经系统低度恶性神经胶质瘤,占所有星形细胞瘤的不到 1%。与其他神经胶质瘤一样,它也可以很少从脑膜中的神经胶质巢中发生,表现为类似于脑膜瘤的外轴性肿块。外轴性 PXA 是一种极为罕见的实体瘤。因此,目前尚无标准化的指南。本文报告了第四例迄今为止的孤立性原发性外轴性 PXA 病例,该患者为 23 岁女性,表现为颞叶癫痫和颅内压升高的特征。通过这个病例,我们试图讨论所有的治疗选择。