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一例罕见的肛周腺泡状横纹肌肉瘤。

A rare case of perianal alveolar rhabdomyosarcoma.

作者信息

Taha Anas, Maeky Amjad, Wentzler Larissa, Taha-Mehlitz Stephanie, Rosenberg Robert, Honaker Michael D

机构信息

Centre for Gastrointestinal surgery Cantonal Hospital Basel-Landschaft Liestal Switzerland.

Department of Surgery East Carolina University, Brody School of Medicine Greenville North Carolina USA.

出版信息

Clin Case Rep. 2024 Sep 12;12(9):e9437. doi: 10.1002/ccr3.9437. eCollection 2024 Sep.

DOI:10.1002/ccr3.9437
PMID:39281027
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC11393001/
Abstract

Perianal alveolar rhabdomyosarcoma is a rare sarcoma that requires a high index of suspicion along with tissue biopsy for accurate diagnosis. Successful treatment, even in the setting of recurrence, requires a multidisciplinary approach.

摘要

肛周肺泡横纹肌肉瘤是一种罕见的肉瘤,准确诊断需要高度的怀疑指数以及组织活检。即使在复发的情况下,成功的治疗也需要多学科方法。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/bac1/11393001/229d3bd0e9e8/CCR3-12-e9437-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/bac1/11393001/2d2637b0f002/CCR3-12-e9437-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/bac1/11393001/8d0bf99a5af1/CCR3-12-e9437-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/bac1/11393001/229d3bd0e9e8/CCR3-12-e9437-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/bac1/11393001/2d2637b0f002/CCR3-12-e9437-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/bac1/11393001/8d0bf99a5af1/CCR3-12-e9437-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/bac1/11393001/229d3bd0e9e8/CCR3-12-e9437-g003.jpg

相似文献

1
A rare case of perianal alveolar rhabdomyosarcoma.一例罕见的肛周腺泡状横纹肌肉瘤。
Clin Case Rep. 2024 Sep 12;12(9):e9437. doi: 10.1002/ccr3.9437. eCollection 2024 Sep.
2
Perianal rhabdomyosarcoma: report of a case in an infant.肛周横纹肌肉瘤:一例婴儿病例报告。
J Pediatr Surg. 1986 Feb;21(2):180-2. doi: 10.1016/s0022-3468(86)80080-x.
3
Perianal and perineal rhabdomyosarcomas: a retrospective multicenter study of 35 cases.肛门和会阴部横纹肌肉瘤:35 例回顾性多中心研究。
BMC Surg. 2021 Jan 30;21(1):66. doi: 10.1186/s12893-021-01073-x.
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Perianal alveolar rhabdomyosarcoma in a child. Report of a long-term survival case.儿童肛周肺泡状横纹肌肉瘤。1例长期生存病例报告。
Dis Colon Rectum. 1983 Nov;26(11):728-31. doi: 10.1007/BF02554984.
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Treatment strategies for perianal rhabdomyosarcoma: report of two cases.肛周横纹肌肉瘤的治疗策略:两例报告
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Perianal rhabdomyosarcoma presenting 21 months after hamartoma excision.错构瘤切除21个月后出现的肛周横纹肌肉瘤。
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Primary alveolar rhabdomyosarcoma of bone.骨原发性肺泡横纹肌肉瘤
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Perianal/perineal rhabdomyosarcoma: Results of the SIOP MMT 95, Italian RMS 96, and EpSSG RMS 2005 studies.肛周/会阴部横纹肌肉瘤:国际小儿肿瘤学会软组织肉瘤研究组95研究、意大利横纹肌肉瘤研究组96研究及欧洲小儿软组织肉瘤研究组2005研究的结果
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Combined management of perianal rhabdomyosarcoma with chemotherapy, radical surgery, and irradiation: A series of three consecutive children.联合化疗、根治性手术和放疗治疗肛周横纹肌肉瘤:连续3例患儿病例系列
J Pediatr Surg. 2019 Feb;54(2):285-287. doi: 10.1016/j.jpedsurg.2018.10.090. Epub 2018 Nov 7.

本文引用的文献

1
Perianal and perineal rhabdomyosarcomas: a retrospective multicenter study of 35 cases.肛门和会阴部横纹肌肉瘤:35 例回顾性多中心研究。
BMC Surg. 2021 Jan 30;21(1):66. doi: 10.1186/s12893-021-01073-x.
2
Surgical management of extremity rhabdomyosarcoma: A consensus opinion from the Children's Oncology Group, the European Pediatric Soft-Tissue Sarcoma Study Group, and the Cooperative Weichteilsarkom Studiengruppe.四肢横纹肌肉瘤的外科治疗:来自儿童肿瘤学组、欧洲儿科软组织肉瘤研究组和软组织肉瘤合作研究组的共识意见。
Pediatr Blood Cancer. 2023 Mar;70(3):e28608. doi: 10.1002/pbc.28608. Epub 2020 Aug 9.
3
Quality assessment of lymph node sampling in rhabdomyosarcoma: A surveillance, epidemiology, and end results (SEER) program study.
横纹肌肉瘤淋巴结采样的质量评估:一项监测、流行病学及最终结果(SEER)项目研究。
J Pediatr Surg. 2017 Apr;52(4):614-617. doi: 10.1016/j.jpedsurg.2016.08.024. Epub 2016 Sep 2.
4
Conservative management of a perianal rhabdomyosarcoma in a 2-year old child by Papillon's technique.采用帕皮永技术对一名2岁儿童的肛周横纹肌肉瘤进行保守治疗。
Radiat Oncol. 2015 May 1;10:108. doi: 10.1186/s13014-015-0413-9.
5
Rhabdomyosarcoma in adolescent and young adult patients: current perspectives.青少年和青年成人患者的横纹肌肉瘤:当前观点
Adolesc Health Med Ther. 2014 Jun 17;5:115-25. doi: 10.2147/AHMT.S44582. eCollection 2014.
6
Classification of rhabdomyosarcoma and its molecular basis.横纹肌肉瘤的分类及其分子基础。
Adv Anat Pathol. 2013 Nov;20(6):387-97. doi: 10.1097/PAP.0b013e3182a92d0d.
7
Treatment and outcome of patients suffering from perineal/perianal rhabdomyosarcoma: results from the CWS trials--retrospective clinical study.会阴/肛周横纹肌肉瘤患者的治疗和转归:CWS 试验的结果——回顾性临床研究。
Ann Surg. 2014 Jun;259(6):1166-72. doi: 10.1097/SLA.0b013e3182a6f320.
8
High incidence of regional and in-transit lymph node metastasis in patients with alveolar rhabdomyosarcoma.肺泡横纹肌肉瘤患者区域及途中淋巴结转移的高发生率。
Int J Clin Oncol. 2014;19(3):536-43. doi: 10.1007/s10147-013-0571-4. Epub 2013 Jun 4.
9
Trends in childhood rhabdomyosarcoma incidence and survival in the United States, 1975-2005.1975 - 2005年美国儿童横纹肌肉瘤的发病率及生存率趋势
Cancer. 2009 Sep 15;115(18):4218-26. doi: 10.1002/cncr.24465.
10
Early experience with PET/CT scan in the evaluation of pediatric abdominal neoplasms.PET/CT扫描在小儿腹部肿瘤评估中的早期经验。
J Pediatr Surg. 2008 Dec;43(12):2186-92. doi: 10.1016/j.jpedsurg.2008.08.064.