Liu Dan, Liu Xiaoge, Li Xin, Liu Yisha, Yu Junlun
Department of Radiology, Sichuan Provincial People's Hospital, University of Electronic Science and Technology of China, Chengdu, China.
Department of Ultrasound, Ya'an People's Hospital, Ya'an, China.
Front Oncol. 2024 Aug 30;14:1431950. doi: 10.3389/fonc.2024.1431950. eCollection 2024.
Extraskeletal Ewing's sarcoma (ES) has been reported to originate from various sites. Primary endobronchial ES is an extremely rare bronchial tumor, especially multifocal lesions. This report describes a rare presentation of primary bronchial ES in a 31-year-old female who was referred to the emergency department of our hospital due to suspicion of a foreign body in the bronchus. Computed tomography and bronchoscopy revealed multiple polypoid nodules in the middle bronchus of her right lung, thus excluding the initial diagnosis. Infection-related laboratory tests and serum tumor markers were normal. The bronchial sleeve resection was performed to remove the tumor completely and the patient's clinical symptoms obviously improved. Subsequent imaging, histopathological, immunohistochemical and genetic analyses made a conclusive diagnosis of primary endobronchial ES. To our knowledge, this is the eighth case of primary bronchial ES reported in medical literature.
据报道，骨外尤因肉瘤（ES）可起源于不同部位。原发性支气管内ES是一种极其罕见的支气管肿瘤，尤其是多灶性病变。本报告描述了一名31岁女性原发性支气管ES的罕见表现，该患者因怀疑支气管内有异物而被转诊至我院急诊科。计算机断层扫描和支气管镜检查显示其右肺中间支气管有多个息肉样结节，从而排除了最初的诊断。感染相关实验室检查和血清肿瘤标志物均正常。进行了支气管袖状切除术以完全切除肿瘤，患者的临床症状明显改善。随后的影像学、组织病理学、免疫组织化学和基因分析确诊为原发性支气管内ES。据我们所知，这是医学文献中报道的第八例原发性支气管ES病例。
