Almaguer Joey, Motamedi Sheedeh, Murray Dylan, Murray Matthew, Murray Richard
Radiology, Texas Tech University Health Sciences Center, Amarillo, USA.
Radiology, Texas Tech University Health Sciences Center, Lubbock, USA.
Cureus. 2024 Aug 18;16(8):e67130. doi: 10.7759/cureus.67130. eCollection 2024 Aug.
Median arcuate ligament syndrome (MALS) is a rare condition in which the median arcuate ligament (MAL) exerts external compression on the celiac trunk. Most cases are asymptomatic and diagnosed incidentally on radiographic imaging; however, some patients may experience gastrointestinal (GI) symptoms related to foregut ischemia and/or celiac neuropathy. In the following case, we present a patient with hemorrhagic peptic ulcer disease of the duodenum, which resulted in episodes of hemodynamic instability requiring multiple blood transfusions. Upon attempted transarterial angioembolization of the gastroduodenal artery (GDA), celiac stenosis and retrograde arterial flow from the superior mesenteric artery confirmed the presence of MALS. This rendered GDA angioembolization a contraindication, as the GDA became the dominant arterial supply for the distal celiac organs. The patient then received open surgical MAL release with concurrent surgical ligation of the hemorrhaging duodenal artery, which resolved his symptoms without the need for further intervention.
正中弓状韧带综合征(MALS)是一种罕见病症,其中正中弓状韧带(MAL)对腹腔干施加外部压迫。大多数病例无症状,在影像学检查时偶然发现;然而,一些患者可能会出现与前肠缺血和/或腹腔神经病变相关的胃肠道(GI)症状。在以下病例中,我们介绍了一名患有十二指肠出血性消化性溃疡疾病的患者,该疾病导致血流动力学不稳定发作,需要多次输血。在尝试对胃十二指肠动脉(GDA)进行经动脉血管栓塞时,腹腔干狭窄以及来自肠系膜上动脉的逆行动脉血流证实了MALS的存在。这使得GDA血管栓塞成为禁忌,因为GDA成为了腹腔干远端器官的主要动脉供应。该患者随后接受了开放性手术正中弓状韧带松解术,并同时对出血的十二指肠动脉进行手术结扎,从而解决了他的症状,无需进一步干预。