Wang Mengzhen, Hu Qiang, Wang Ni, Jiang Yuge, Dong Ting, Cao Shijian, Zhou An
School of Pharmacy, Anhui University of Chinese Medicine, Hefei, 230038, China.
Key Laboratory of Xin'an Medicine of the Ministry of Education, Hefei, 230038, China.
Biol Trace Elem Res. 2024 Sep 21. doi: 10.1007/s12011-024-04384-1.
Wilson's disease (WD) is an inherited disorder that is characterized by abnormal copper metabolism, and treatment of this condition in the clinic focuses on promoting copper ion excretion. Glutathione (GSH) is a tripeptide compound whose active group is a sulfhydryl group, which is involved in many important biochemical reactions. Thus, the antioxidant and integrative detoxification effects of GSH have attracted attention. Whether GSH promotes copper ion excretion and reduces oxidative stress to alleviate WD-related liver injury is the focus of this study. Here, we used toxic milk (TX) mice as a model to study WD, and we treated these mice with GSH. We observed that GSH was effective at promoting copper excretion by TX mice. In addition, GSH has been shown to be effective in attenuating liver injury, including improving the structure and morphology of stem tissue and reducing hepatocyte necrosis. The effects of GSH on hepatic oxidative stress were determined by measuring catalase, malondialdehyde and total superoxide dismutase. The results showed that GSH could increase hepatic antioxidant enzyme activities, reduce lipid peroxidation levels and attenuate liver injury. In conclusion, GSH may exert its hepatic benefits by promoting copper ion excretion and preventing oxidative stress.
威尔逊病(WD)是一种遗传性疾病,其特征为铜代谢异常,临床治疗该疾病的重点是促进铜离子排泄。谷胱甘肽(GSH)是一种三肽化合物,其活性基团为巯基,参与许多重要的生化反应。因此,GSH的抗氧化和综合解毒作用受到关注。GSH是否能促进铜离子排泄并减轻氧化应激以缓解WD相关的肝损伤是本研究的重点。在此,我们使用毒奶(TX)小鼠作为模型来研究WD,并对这些小鼠进行GSH治疗。我们观察到GSH能有效促进TX小鼠排泄铜。此外,GSH已被证明能有效减轻肝损伤,包括改善肝组织的结构和形态以及减少肝细胞坏死。通过测量过氧化氢酶、丙二醛和总超氧化物歧化酶来确定GSH对肝脏氧化应激的影响。结果表明,GSH可增加肝脏抗氧化酶活性,降低脂质过氧化水平并减轻肝损伤。总之,GSH可能通过促进铜离子排泄和预防氧化应激来发挥其对肝脏的益处。