McDermott W V, Topol B M
J Surg Oncol. 1985 Dec;30(4):221-5. doi: 10.1002/jso.2930300407.
A case of systemic mastocytosis is reported with an observation period of 20 years. During these two decades multiple manifestations of the disease appeared including urticaria pigmentosis, episodic histamine release, gastro-intestinal involvement and hepatosplenomegaly. The most extraordinary, and possibly unique phenomenon, has been the development of a massive proliferation of large mastocytomas mainly, but not exclusively, limited to the lower extremities. For different reasons (mechanical disability, bleeding, cosmesis), these tumors have required repeated admissions for surgical removal. The most successful technique has involved use of the ultrasonic scalpel.
报告了一例系统性肥大细胞增多症病例，观察期为20年。在这二十年中，该疾病出现了多种表现，包括色素性荨麻疹、组胺的间歇性释放、胃肠道受累和肝脾肿大。最不寻常且可能独特的现象是主要但不仅限于下肢出现大量大的肥大细胞瘤增殖。由于不同原因（机械性残疾、出血、美容），这些肿瘤需要多次入院进行手术切除。最成功的技术是使用超声刀。
