Gattani Preeti, Heda Sakshi, Kedar Aarzoo S, Zade Rasika D, Gattani Rajesh G
Obstetrics and Gynaecology, Datta Meghe Medical College, Datta Meghe Institute of Higher Education and Research (Deemed to be University), Wardha, IND.
Obstetrics and Gynaecology, All India Institute of Medical Sciences, Rishikesh, IND.
Cureus. 2024 Sep 4;16(9):e68680. doi: 10.7759/cureus.68680. eCollection 2024 Sep.
Congenital clitoromegaly, also known as macroclitoris, is a rare congenital disorder. It is a cause of poor self-esteem, anxiety, and gender self-perception. It negatively affects social, romantic, and emotional domains. We present a case of female pseudohermaphroditism with congenital clitoromegaly in a 23-year-old woman who attained late menarche at 22 years of age. Her karyotype was normal (46XX). She had clitoromegaly and a small vaginal opening with labial fusion and scrotalization. We performed feminizing genitoplasty, which included neurovascular sparing clitoroplasty, labioplasty, and vaginoplasty. Follow-up after two weeks revealed feminine genitalia. She is delighted as her ambiguity has been corrected with a good cosmetic effect and is satisfied with the aesthetics, sexual arousal, and self-esteem.
先天性阴蒂肥大，也称为巨阴蒂，是一种罕见的先天性疾病。它是导致自尊低下、焦虑和性别自我认知问题的一个原因。它对社交、恋爱和情感领域产生负面影响。我们报告一例23岁女性先天性阴蒂肥大的女性假两性畸形病例，该患者22岁月经初潮较晚。她的核型正常（46XX）。她有阴蒂肥大、小阴道口、阴唇融合和阴囊化。我们进行了女性化生殖器成形术，包括保留神经血管的阴蒂成形术、阴唇成形术和阴道成形术。两周后的随访显示生殖器呈女性化。她很高兴，因为她的两性畸形已得到矫正，美容效果良好，对美观、性唤起和自尊都很满意。
