Jarrar Saba' A, Altamimi Shawkat, Hasweh Reem
Otolaryngology, Al-Balqa Applied University, Al-Salt, JOR.
Radiology, Al-Balqa Applied University, Al-Salt, JOR.
Cureus. 2024 Sep 30;16(9):e70509. doi: 10.7759/cureus.70509. eCollection 2024 Sep.
Sjögren's syndrome (SS) is an autoimmune disorder that usually affects middle-aged females. Juvenile SS is of unknown prevalence. The classic presenting symptoms in adults are mouth and eye dryness, while in children and adolescents, recurrent parotitis is more often the presenting symptom with the absence of sicca symptoms. We present the case of a 17-year-old girl with recurrent bilateral parotid swelling for the last eight months. The parotid CT scan showed prominent parotid glands associated with multiple tiny calcifications and cyst formation. Serologic studies showed significantly elevated Ro/SSA antibodies. A lip biopsy showed periductal lymphocytic infiltration. As the patient fulfilled the diagnostic criteria for SS, she was subsequently referred to a rheumatologist for specialized management. This report aims to focus on the variation in the presentation of SS in younger age groups among different specialties that deal with these cases initially and to diagnose SS as early as possible to improve the outcome and reduce complications.
干燥综合征（SS）是一种通常影响中年女性的自身免疫性疾病。青少年干燥综合征的患病率尚不清楚。成年人典型的首发症状是口干和眼干，而在儿童和青少年中，复发性腮腺炎更常作为首发症状，且无干燥症状。我们报告一例17岁女孩，在过去八个月中反复出现双侧腮腺肿大。腮腺CT扫描显示腮腺肿大，伴有多个微小钙化和囊肿形成。血清学研究显示Ro/SSA抗体显著升高。唇腺活检显示导管周围淋巴细胞浸润。由于该患者符合干燥综合征的诊断标准，随后被转诊至风湿病专家处进行专科治疗。本报告旨在关注不同专科在最初处理这些病例时，年轻年龄组干燥综合征临床表现的差异，并尽早诊断干燥综合征以改善预后和减少并发症。
