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以呼吸困难和咯血为表现的白塞病:一例肺动脉瘤病例报告

Dyspnea and hemoptysis revealing Behçet's syndrome: Pulmonary artery aneurysms in a case report.

作者信息

Ez-Zaky Sara, Laasri Ihssane, Jroundi Laila, Laamrani Fatima Zahra

机构信息

Emergency Radiology Department, Ibn Sina University Hospital Center, Mohammed V University, Rabat, Morocco.

出版信息

Radiol Case Rep. 2024 Oct 14;20(1):115-118. doi: 10.1016/j.radcr.2024.09.110. eCollection 2025 Jan.

Abstract

Behçet's disease is a systemic vasculitis that primarily affects young adults. Arterial involvement in Behçet's disease is rare and associated with a poor prognosis. This manifestation is rarely the initial presentation, often leading to a delayed diagnosis. We present the case of a 27-year-old man who arrived at the emergency department with dyspnea and hemoptysis. An initial chest X-ray revealed bilateral opacities, and subsequent thoracic CT angiography confirmed the presence of pulmonary artery aneurysms. Pulmonary artery involvement, though rare, is a serious condition that manifests as hemoptysis (airway bleeding) caused by pulmonary aneurysms. These aneurysms, often challenging to diagnose, can result in severe hemorrhages and carry a low 2-year survival rate. CT pulmonary angiography is the most effective imaging method for identifying thoracic manifestations of Behçet's disease. Treatment includes early immunosuppression, surgery, or embolization in severe cases, such as those involving massive hemoptysis.

摘要

白塞病是一种主要影响年轻成年人的系统性血管炎。白塞病累及动脉的情况罕见,且预后不良。这种表现很少是首发症状,常常导致诊断延迟。我们报告一例27岁男性病例,该患者因呼吸困难和咯血到急诊科就诊。最初的胸部X线检查显示双侧肺部有阴影,随后的胸部CT血管造影证实存在肺动脉瘤。肺动脉受累虽然罕见,但却是一种严重的病症,表现为由肺动脉瘤引起的咯血(气道出血)。这些动脉瘤常常难以诊断,可导致严重出血,2年生存率较低。CT肺动脉造影是识别白塞病胸部表现的最有效影像学方法。治疗包括早期免疫抑制,对于严重病例如出现大量咯血的情况可进行手术或栓塞治疗。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7253/11526055/8f09c4cb82c6/gr1.jpg

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