Houssem Messaoudi, Habib Bessrour, Wafa Raghmoun, Syrine Dardour, Nada Mansouri, Saber Hachicha
Department of Cardiothoracic Surgery, The Principal Military Hospital of Instruction of Tunis, Tunisia.
Department of Cardiothoracic Surgery, The Principal Military Hospital of Instruction of Tunis, Tunisia.
Int J Surg Case Rep. 2024 Dec;125:110544. doi: 10.1016/j.ijscr.2024.110544. Epub 2024 Oct 30.
Glomangioma is an uncommon hypervascular tumor typically found in the extremities, with primary occurrences in the mediastinum being exceedingly rare.
A 38-year-old male presented to our cardio-thoracic surgery department with chest pain. Chest computed tomography (CT) revealed a 45 mm posterior paravertebral right solidocystic mass, a finding confirmed by Magnetic resonance imaging (MRI) with a solidocystic mass in the posterior paravertebral right pleura suggesting a fibrous tumor exhibiting cystic degeneration. Surgical intervention under right thoracotomy involved the complete resection of the tumor. Postoperative analysis confirmed the diagnosis of a glomus tumor.
Glomus tumors are uncommon growths that arise from neuromyoarterial glomus bodies, which are specialized structures involved in regulating blood flow and skin surface temperature through arteriovenous connections. Our case represents the ninth instance of a glomus tumor in the mediastinum. The clinical manifestation of intrathoracic glomus tumors lacks specificity and can vary depending on the location and size of the tumor, often resembling typical thoracic tumors. Surgical resection remains the foremost approach for diagnosing and treating thoracic glomus tumors. Given the potential for malignancy, a radical resection is advised to ensure complete removal with clear margins.
This case describes an uncommon presentation of a benign glomus tumor in the posterior mediastinum, highlighting its exceptional localization and emphasizing the critical importance of surgical resection for optimal management.
血管球瘤是一种罕见的高血管性肿瘤,通常发生于四肢,原发性纵隔血管球瘤极为罕见。
一名38岁男性因胸痛就诊于我院心胸外科。胸部计算机断层扫描(CT)显示右椎旁后方有一个45毫米的实性囊性肿块,磁共振成像(MRI)证实了这一发现,右椎旁胸膜后方的实性囊性肿块提示为囊性退变的纤维瘤。在右胸切开术下行手术干预,完整切除了肿瘤。术后分析确诊为血管球瘤。
血管球瘤是起源于神经肌动脉血管球的罕见肿瘤,血管球是通过动静脉连接参与调节血流和皮肤表面温度的特殊结构。我们的病例是纵隔血管球瘤的第九例。胸内血管球瘤的临床表现缺乏特异性,可因肿瘤的位置和大小而异,常类似典型的胸部肿瘤。手术切除仍然是诊断和治疗胸内血管球瘤的首要方法。鉴于有恶变的可能,建议行根治性切除以确保切缘清晰完整切除。
本病例描述了后纵隔良性血管球瘤的罕见表现,突出了其特殊的定位,并强调了手术切除对最佳治疗的至关重要性。