Bautista Catherine H, Chen Joanna, Ormiston Laurel, Moore Zachary J, Husain Adil, Gociman Barbu
From the Division of Plastic and Reconstructive Surgery, Department of Surgery, University of Utah School of Medicine, Salt Lake City, Utah.
Division of Cardiothoracic Surgery, Department of Surgery, University of Utah, Salt Lake City, Utah.
Plast Reconstr Surg Glob Open. 2024 Nov 18;12(11):e6299. doi: 10.1097/GOX.0000000000006299. eCollection 2024 Nov.
Ectopia cordis is a rare congenital condition resulting in extrathoracic positioning of the heart. The severity of presentation may vary with partial or complete displacement through sternal or diaphragmatic defects. Operative management is typically required, but due to the rarity of the condition, no standard exists for optimal closure. Reconstruction techniques can include compound local flap placement including pectoralis major, rectus abdominis, or latissimus dorsi flaps as well as synthetic material placement, autologous bone, and cartilage grafts to correct sternal deformity. This case report outlines the successful utilization of bilateral composite pectoralis major and rectus abdominal musculocutaneous flaps for complex staged closure of a sternal wound after creation of a cavopulmonary anastomosis in a 5-year-old patient with concomitant single-ventricle congenital heart disease. This single-staged closure after cardiac repair was performed without intra- or postoperative complications, and the patient demonstrated satisfactory healing with stable cardiac coverage at follow-up visit. This technique may present as an effective approach in complex sternal wound closure in patients with ectopia cordis.
心脏异位是一种罕见的先天性疾病,导致心脏位于胸腔外。临床表现的严重程度可能因通过胸骨或膈肌缺损的部分或完全移位而有所不同。通常需要进行手术治疗,但由于这种疾病的罕见性,尚无最佳闭合的标准。重建技术可包括复合局部皮瓣移植,如胸大肌、腹直肌或背阔肌皮瓣,以及合成材料植入、自体骨和软骨移植以纠正胸骨畸形。本病例报告概述了在一名患有单心室先天性心脏病的5岁患者中,在进行腔肺吻合术后,成功利用双侧复合胸大肌和腹直肌肌皮瓣对胸骨伤口进行复杂的分期闭合。心脏修复后的这种单期闭合手术未出现术中或术后并发症,患者在随访时显示愈合良好,心脏覆盖稳定。该技术可能是心脏异位患者复杂胸骨伤口闭合的有效方法。