Lampert Joshua A, Harmaty Marco, Thompson Elizabeth Chabner, Sett Suvro, Koch R Michael
Division of Plastic and Reconstructive Surgery, New York Medical College, Maria Fareri Children's Hospital, Valhalla, NY, USA.
Ann Plast Surg. 2010 Nov;65(5):485-9. doi: 10.1097/SAP.0b013e3181d376a3.
Ectopia cordis is a rare congenital defect characterized by complete or partial displacement of the heart outside the thoracic cavity. Repair of ectopia cordis can present a reconstructive challenge often requiring a staged approach. Ideally, structural integrity and protection of the heart are restored using autologous tissues capable of growth. In addition, reconstruction of the thorax must proceed without compromise to pulmonary or cardiovascular stability. The following article describes repair of thoracoabdominal ectopia cordis in a patient with pentalogy of Cantrell. Reconstruction of the chest wall was accomplished using a musculoosseus composite flap involving segments of the 9th and 10th ribs and overlying pedicled latissimus dorsi muscle. This is the first report known to the authors of such a repair.
心脏异位是一种罕见的先天性缺陷，其特征是心脏完全或部分移位至胸腔外。心脏异位的修复可能带来重建挑战，通常需要分阶段进行。理想情况下，使用能够生长的自体组织来恢复心脏的结构完整性并提供保护。此外，胸廓重建必须在不损害肺或心血管稳定性的情况下进行。以下文章描述了一名患有坎特雷尔五联症患者的胸腹型心脏异位的修复。胸壁重建采用了一种肌肉骨骼复合瓣，该瓣包含第9和第10肋骨段以及覆盖其上的带蒂背阔肌。这是作者所知的关于此类修复的首例报告。
