Daher Y H, Lonstein J E, Winter R B, Bradford D S
Clin Orthop Relat Res. 1986 Jan(202):219-22.
Twelve patients with Charcot-Marie-Tooth disease and scoliosis, seven girls and five boys (average age at presentation, ten years), were investigated for an average of 49 months. All but one of the patients were ambulatory. The curve patterns were thoracic in two, thoracolumbar in four, and double thoracic and lumbar curves in six. There was an associated kyphosis in six. Three patients had brace treatment with curve control in two. Four patients underwent posterior spinal fusion with Harrington instrumentation, one with segmental sublaminar wires. Post-operative management consisted of a cast for one patient and a brace for the remaining three. Follow-up period in the surgical patients ranged from 19 to 45 months (average, 32 months). One patient had a superior mesenteric artery syndrome and two had a pseudarthrosis.
12例患有夏科-马里-图思病和脊柱侧凸的患者(7名女孩和5名男孩,就诊时平均年龄为10岁)接受了平均49个月的调查。除1例患者外,所有患者均可行走。曲线类型为2例胸椎型、4例胸腰段型、6例双胸腰段型。6例伴有后凸畸形。3例患者接受支具治疗,其中2例曲线得到控制。4例患者接受了哈灵顿器械后路脊柱融合术,1例采用节段性椎板下钢丝固定。术后管理方面,1例患者使用石膏,其余3例使用支具。手术患者的随访期为19至45个月(平均32个月)。1例患者出现肠系膜上动脉综合征,2例出现假关节。