Martins José Diogo, Soares Catarina, Barreiros Cátia, Teixeira Filipa, Ferreira Manuel
Internal Medicine, Unidade Local de Saúde do Alto Minho, Viana do Castelo, PRT.
Rheumatology, Unidade Local de Saúde do Alto Minho, Viana do Castelo, PRT.
Cureus. 2024 Oct 19;16(10):e71834. doi: 10.7759/cureus.71834. eCollection 2024 Oct.
Granulomatosis with polyangiitis (GPA), formerly known as Wegener's granulomatosis, is a rare autoimmune disorder characterized by necrotizing vasculitis affecting small to medium-sized vessels. This condition most commonly affects the lungs, kidneys, and upper respiratory tract. Early recognition and treatment are critical to prevent severe complications and improve prognosis. This report presents the case of a 48-year-old male with GPA, with primary pulmonary and articular involvement, who presented with respiratory symptoms and was initially misdiagnosed as having pulmonary tuberculosis due to cavitary lesions on imaging.
肉芽肿性多血管炎(GPA),以前称为韦格纳肉芽肿,是一种罕见的自身免疫性疾病,其特征是坏死性血管炎,影响中小血管。这种疾病最常累及肺部、肾脏和上呼吸道。早期识别和治疗对于预防严重并发症和改善预后至关重要。本报告介绍了一名48岁患有GPA的男性病例,主要累及肺部和关节,该患者出现呼吸道症状,最初因影像学上的空洞性病变被误诊为肺结核。