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迁移性空洞形成作为肉芽肿性多血管炎某一特定病例的主要受累表现。

Migrant cavitation as primary involvement in a particular case of granulomatosis with polyangiitis.

作者信息

Manti Francesco, Battaglia Caterina, Pelaia Corrado, Petullà Maria, Bertucci Bernardo, Laganà Domenico

机构信息

Radiodiagnostic Institute, "Magna Græcia" University of Catanzaro, Catanzaro, Italy.

Respiratory Medicine Unite, "Magna Græcia" University of Catanzaro, Catanzaro, Italy.

出版信息

Radiol Case Rep. 2022 Jul 28;17(10):3535-3538. doi: 10.1016/j.radcr.2022.06.074. eCollection 2022 Oct.

DOI:10.1016/j.radcr.2022.06.074
PMID:35923342
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC9340142/
Abstract

Granulomatosis with polyangiitis (GPA), previously known as Wegener's granulomatosis, is a necrotizing granulomatous vasculitis of the small and medium vessels involving the upper respiratory tract, lungs, and kidneys. In this case report, we will describe the case of a 60-year-old man who presented to our observation with recurrent episodes of hemoptoe, fever, and mucopurulent sputum. The diagnosis was made by radiological and laboratory tests.

摘要

肉芽肿性多血管炎(GPA),以前称为韦格纳肉芽肿,是一种累及上呼吸道、肺和肾脏的中小血管坏死性肉芽肿性血管炎。在本病例报告中,我们将描述一名60岁男性的病例,该患者因反复咯血、发热和黏液脓性痰前来我院就诊。诊断通过影像学和实验室检查做出。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e5b6/9340142/8c5e658c2958/gr5.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e5b6/9340142/7c64207bdc43/gr1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e5b6/9340142/87e9ea2f0a4a/gr2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e5b6/9340142/6ceef653a0a9/gr3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e5b6/9340142/3cb95220414a/gr4.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e5b6/9340142/8c5e658c2958/gr5.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e5b6/9340142/7c64207bdc43/gr1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e5b6/9340142/87e9ea2f0a4a/gr2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e5b6/9340142/6ceef653a0a9/gr3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e5b6/9340142/3cb95220414a/gr4.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e5b6/9340142/8c5e658c2958/gr5.jpg

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本文引用的文献

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2022 American College of Rheumatology/European Alliance of Associations for Rheumatology Classification Criteria for Granulomatosis With Polyangiitis.2022 年美国风湿病学会/欧洲风湿病联盟肉芽肿性多血管炎分类标准。
Arthritis Rheumatol. 2022 Mar;74(3):393-399. doi: 10.1002/art.41986. Epub 2022 Feb 2.
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ANCA-associated vasculitis.抗中性粒细胞胞浆抗体相关性血管炎。
Nat Rev Dis Primers. 2020 Aug 27;6(1):71. doi: 10.1038/s41572-020-0204-y.
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Imaging in Vasculitis.血管炎的影像学表现
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Clinical associations of renal involvement in ANCA-associated vasculitis.肾血管炎相关抗中性粒细胞胞质抗体相关性血管炎的临床相关性。
Autoimmun Rev. 2020 Apr;19(4):102495. doi: 10.1016/j.autrev.2020.102495. Epub 2020 Feb 15.
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Antineutrophil Cytoplasmic Antibodies Testing and Interpretation.抗中性粒细胞胞浆抗体检测与解读
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The clinical presentation and therapy of diseases related to anti-neutrophil cytoplasmic antibodies (ANCA).与抗中性粒细胞胞浆抗体(ANCA)相关疾病的临床表现和治疗。
Autoimmun Rev. 2016 Oct;15(10):978-82. doi: 10.1016/j.autrev.2016.07.016. Epub 2016 Jul 29.
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Clinic manifestations in granulomatosis with polyangiitis.肉芽肿性多血管炎的临床表现。
Int J Immunopathol Pharmacol. 2016 Jun;29(2):151-9. doi: 10.1177/0394632015617063. Epub 2015 Dec 18.
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Pulmonary vasculitis.肺血管炎
Rheum Dis Clin North Am. 2015 May;41(2):315-31. doi: 10.1016/j.rdc.2015.01.004. Epub 2015 Feb 27.
9
Granulomatosis with polyangiitis (Wegener): clinical aspects and treatment.肉芽肿性多血管炎(韦格纳):临床特征和治疗。
Autoimmun Rev. 2014 Nov;13(11):1121-5. doi: 10.1016/j.autrev.2014.08.017. Epub 2014 Aug 20.
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Diagnosis and classification of granulomatosis with polyangiitis (aka Wegener's granulomatosis).肉芽肿性多血管炎(又名韦格纳氏肉芽肿病)的诊断和分类。
J Autoimmun. 2014 Feb-Mar;48-49:94-8. doi: 10.1016/j.jaut.2014.01.028. Epub 2014 Jan 29.