Ullah Muhammad Khubaib, Khan Faheemullah, Aman Muhammad, Zafar Uffan, Irfan Muhammad, Khandwala Kumail, Nadeem Naila, Ahmad Izaz, Nadeem Arsalan, Khan Noman
Ayub Medical College Abbottabad Pakistan.
Cleveland Clinic Main Campus Cleveland Ohio USA.
Clin Case Rep. 2024 Nov 29;12(12):e9662. doi: 10.1002/ccr3.9662. eCollection 2024 Dec.
In the pediatric age group, FXIII deficiency can present as abnormal or delayed bleeding from the umbilical stump, soft tissue and subcutaneous bleeding, intracerebral hemorrhages, intraoral bleeding, and poor wound healing. This case report describes an atypical presentation of FXIII deficiency in a 3-year-old female who presented to the emergency department with complaints of abdominal pain and vomiting. She was managed conservatively under the care of the pediatric surgery team.
在儿童年龄组中,凝血因子ⅩⅢ缺乏症可表现为脐带残端异常出血或出血延迟、软组织和皮下出血、脑出血、口腔内出血以及伤口愈合不良。本病例报告描述了一名3岁女性凝血因子ⅩⅢ缺乏症的非典型表现,该患者因腹痛和呕吐主诉就诊于急诊科。她在小儿外科团队的护理下接受了保守治疗。