Lee Yoonjae, Park Moo Kyun, Lee Jun Ho, Lee Sang-Yeon, Suh Myung-Whan
Department of Otorhinolaryngology-Head and Neck Surgery, Seoul National University Hospital, Seoul, Korea.
Sensory Organ Research Institute, Seoul National University Medical Research Center, Seoul, Korea.
Clin Exp Otorhinolaryngol. 2025 Feb;18(1):14-20. doi: 10.21053/ceo.2024.00189. Epub 2024 Dec 2.
Congenital aural atresia (CAA) is a complex condition that manifests in various forms, including Schuknecht type B stenosis, which is characterized by a congenitally narrow bony external auditory canal (EAC). This study aims to evaluate the long-term surgical outcomes of canal-tympanoplasty in patients with Schuknecht type B CAA.
The study included 21 ears diagnosed with Schuknecht type B CAA, all of which underwent canal-tympanoplasty. Reconstruction of the large EAC and tympanic membrane involved conchal flap meatoplasty, bony EAC drilling, ossicular reconstruction, and overlay tympanoplasty. Standard pure-tone audiometry was analyzed at multiple post-surgery time points: 3, 6, 12, and 24-60 months. Additionally, the incidence of postoperative complications was assessed.
The hearing outcomes of canal-tympanoplasty in this case series were satisfactory. Serviceable hearing was achieved in all patients after 3 months and was maintained in 85% of patients for 1 year. The air-bone gap improved from a preoperative average of 39.3±15.1 dB to 13.7±7.4 dB at 3 months, 16.4±10.5 dB at 6 months, 19.1±11.7 dB at 12 months, and 21.5±16.1 dB at 2-5 years postoperatively. Three patients required revision canal-tympanoplasty due to hearing deterioration, representing 14.3% of the cases. There were no instances of postoperative infection, facial nerve weakness, vertigo, deterioration of bone conduction thresholds, or complete restenosis of the EAC.
Canal-tympanoplasty proved to be a satisfactory surgical intervention for patients with Schuknecht type B CAA. This procedure led to significant improvements in hearing outcomes, providing serviceable hearing that lasted for several years. Moreover, the risk of postoperative hearing deterioration and/or the need for revision surgery within 1 year was considered acceptable.
先天性外耳道闭锁(CAA)是一种复杂的病症,有多种表现形式,包括舒克内希特B型狭窄,其特征为先天性骨性外耳道(EAC)狭窄。本研究旨在评估舒克内希特B型CAA患者行外耳道鼓室成形术的长期手术效果。
该研究纳入了21例诊断为舒克内希特B型CAA的耳,均接受了外耳道鼓室成形术。大外耳道和鼓膜的重建包括耳甲腔瓣成形术、骨性外耳道钻孔、听骨链重建和覆盖式鼓室成形术。在术后多个时间点进行标准纯音听力测定:3个月、6个月、12个月以及24至60个月。此外,评估术后并发症的发生率。
本病例系列中外耳道鼓室成形术的听力结果令人满意。所有患者在3个月后均获得了可用听力,85%的患者在1年内维持了该听力水平。气骨导差从术前平均39.3±15.1 dB改善至术后3个月时的13.7±7.4 dB、6个月时的16.4±10.5 dB、12个月时的19.1±11.7 dB以及术后2至5年时的21.5±16.1 dB。3例患者因听力下降需要进行外耳道鼓室成形术翻修,占病例的14.3%。未发生术后感染、面神经麻痹、眩晕、骨导阈值恶化或外耳道完全再狭窄的情况。
外耳道鼓室成形术被证明是治疗舒克内希特B型CAA患者的一种令人满意的手术干预方法。该手术使听力结果得到显著改善,提供了持续数年的可用听力。此外,术后1年内听力下降和/或需要翻修手术的风险被认为是可接受的。