Zhonghua Xue Ye Xue Za Zhi. 2024 Oct 14;45(10):889-896. doi: 10.3760/cma.j.cn121090-20240809-00296.
Hemophilia is a X-linked recessive hemorrhagic disease. Bleeding is the most common complication of hemophilia, and it is also the main cause leading to death and disability or reducing the quality of life of hemophilia patients. Rapid identification and standardized management of the bleeding events is of great significance to improve the prognosis of hemophilia patients. Emergency department is the frontline department for hemophilia patients with bleeding. The emergent management process of hemophilia hemorrhage is complex and often needs multidisciplinary team cooperation. To increase the awareness of the related professionals who may involve in the management of bleeding events of hemophilia patients, in collaboration with the Thrombosis and Hemostasis Group, Chinese Society of Hematology, Chinese Medical Association, Hemophilia Treatment Center Collaborative Network of China issued the Chinese guidelines for emergency management of bleeding in hemophilia patients.
血友病是一种X连锁隐性出血性疾病。出血是血友病最常见的并发症,也是导致血友病患者死亡、残疾或生活质量下降的主要原因。快速识别并规范处理出血事件对改善血友病患者的预后具有重要意义。急诊科是血友病出血患者的一线科室。血友病出血的紧急处理过程复杂,常需多学科团队协作。为提高可能参与血友病患者出血事件管理的相关专业人员的认识,中国医学协会血液学分会血栓与止血学组联合中国血友病治疗中心协作网络发布了《血友病患者出血的紧急处理中国指南》。