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女童远端尿道重复畸形:一例合并憩室成分的独特病例报告。

Distal Urethral Duplication in a Female Child: A Unique Case Report with Diverticular Component.

作者信息

Arkan Gokhan, Kaya Cem, Turker Leyla Nur, Aracıer Ucaner Fatma Nur, Karabulut Ramazan, Turkyilmaz Zafer, Sonmez Kaan

机构信息

Department of Pediatric Surgery, Gazi University Faculty of Medicine, Ankara, Turkey.

Department of Pediatric Surgery, Gazi University Faculty of Medicine, Ankara, Turkey.

出版信息

J Pediatr Adolesc Gynecol. 2025 Jun;38(3):419-421. doi: 10.1016/j.jpag.2024.12.006. Epub 2024 Dec 7.

DOI:10.1016/j.jpag.2024.12.006
PMID:39653112
Abstract

STUDY OBJECTIVE

To report a rare case of urethral duplication (UD) in a 5-year-9-month-old girl and describe the surgical approach and outcomes.

METHODS

A 5-year-9-month-old girl presented with postvoid dribbling and clitoral swelling. Physical examination and imaging were performed. During surgery, a fistula tract was identified, dissected, and excised. This tract was found to be a UD extending between the distal urethra and the clitoris. The procedure involved advancing a polypropylene suture through the fistula and observing its course via cystoscopy.

RESULTS

The fistula tract was successfully excised, resolving both the clitoral swelling and dribbling. The patient recovered without complications and showed no recurrence at the 2-month follow-up.

CONCLUSION

UD, though exceedingly rare in females, should be considered in cases of urinary incontinence. Surgical excision is an effective treatment with favorable outcomes.

摘要

研究目的

报告一例5岁9个月女童罕见的尿道重复畸形(UD)病例,并描述手术方法及结果。

方法

一名5岁9个月女童出现排尿后滴尿和阴蒂肿胀症状。进行了体格检查和影像学检查。手术过程中,识别、分离并切除了一条瘘管。发现该瘘管是一条在远端尿道和阴蒂之间延伸的尿道重复畸形。手术步骤包括将一根聚丙烯缝线穿过瘘管,并通过膀胱镜观察其走行。

结果

瘘管成功切除,阴蒂肿胀和滴尿问题均得到解决。患者恢复过程中无并发症,在2个月的随访中未出现复发。

结论

尿道重复畸形在女性中极为罕见,但在尿失禁病例中应予以考虑。手术切除是一种有效的治疗方法,效果良好。

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