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伴1型反应的界线类偏瘤型麻风:1例具有挑战性的诊断病例

Borderline Lepromatous Leprosy With Type 1 Reaction: A Challenging Diagnostic Case.

作者信息

Saray Polanco Llanes Alondra, Dalit Zajdman Faitelson, Itzel Figueroa Basurto Carla, Montserrat Rodríguez Escamilla Irene, Elisa Vega Memije María, Roberto Arenas Guzmán

机构信息

National Autonomous University of Mexico Mexico City Mexico.

Dermatology Department "Manuel Gea Gonzalez" General Hospital Mexico City Mexico.

出版信息

Clin Case Rep. 2024 Dec 10;12(12):e9697. doi: 10.1002/ccr3.9697. eCollection 2024 Dec.

DOI:10.1002/ccr3.9697
PMID:39664739
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC11631788/
Abstract

Borderline lepromatous leprosy with Type 1 reaction poses significant diagnostic challenges due to overlapping clinical features. Early recognition and differentiation are crucial, especially in endemic regions like Mexico, to ensure prompt, appropriate management and prevent complications. Accurate diagnosis requires a multidisciplinary approach integrating clinical, histopathological, and microbiological data.

摘要

伴有1型反应的界线类偏瘤型麻风由于临床特征重叠而带来重大诊断挑战。早期识别和鉴别至关重要,尤其在墨西哥等流行地区,以确保及时、恰当的管理并预防并发症。准确诊断需要采用综合临床、组织病理学和微生物学数据的多学科方法。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3e67/11631788/5800152d7dd3/CCR3-12-e9697-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3e67/11631788/4faaa52f2c98/CCR3-12-e9697-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3e67/11631788/afcb245a963a/CCR3-12-e9697-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3e67/11631788/5800152d7dd3/CCR3-12-e9697-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3e67/11631788/4faaa52f2c98/CCR3-12-e9697-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3e67/11631788/afcb245a963a/CCR3-12-e9697-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3e67/11631788/5800152d7dd3/CCR3-12-e9697-g003.jpg

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本文引用的文献

1
Leprosy Caused by Mycobacterium lepromatosis.由瘤型麻风分枝杆菌引起的麻风病。
Am J Clin Pathol. 2022 Dec 1;158(6):678-686. doi: 10.1093/ajcp/aqac110.
2
Mycobacterium leprae: Pathogenesis, diagnosis, and treatment options.麻风分枝杆菌:发病机制、诊断和治疗选择。
Microb Pathog. 2020 Dec;149:104475. doi: 10.1016/j.micpath.2020.104475. Epub 2020 Sep 12.
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Borderline Lepromatous Leprosy: Uncommon Clinical Presentation.
Am J Dermatopathol. 2019 Mar;41(3):211-213. doi: 10.1097/DAD.0000000000001262.
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Leprosy - an overview of clinical features, diagnosis, and treatment.麻风病——临床特征、诊断和治疗概述。
J Dtsch Dermatol Ges. 2017 Aug;15(8):801-827. doi: 10.1111/ddg.13301.
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Histopathology of the lepromatous skin biopsy.麻风性皮肤活检的组织病理学
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Recognizing and managing the immunologic reactions in leprosy.认识和管理麻风病中的免疫反应。
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Leprosy. An update: definition, pathogenesis, classification, diagnosis, and treatment.麻风病。最新进展:定义、发病机制、分类、诊断及治疗
Actas Dermosifiliogr. 2013 Sep;104(7):554-63. doi: 10.1016/j.adengl.2012.03.028. Epub 2013 Jul 17.
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Human beta-defensin 3 is up-regulated in cutaneous leprosy type 1 reactions.人β-防御素 3 在 1 型麻风反应性皮损中呈上调表达。
PLoS Negl Trop Dis. 2012;6(11):e1869. doi: 10.1371/journal.pntd.0001869. Epub 2012 Nov 1.
9
Hansen's disease (Leprosy): current and future pharmacotherapy and treatment of disease-related immunologic reactions.汉森病(麻风病):当前和未来的药物治疗和治疗相关免疫反应的疾病。
Pharmacotherapy. 2012 Jan;32(1):27-37. doi: 10.1002/PHAR.1009.
10
Cytokine and protein markers of leprosy reactions in skin and nerves: baseline results for the North Indian INFIR cohort.麻风反应中皮肤和神经的细胞因子和蛋白标志物:印度北部 INFIR 队列的基线结果。
PLoS Negl Trop Dis. 2011 Dec;5(12):e1327. doi: 10.1371/journal.pntd.0001327. Epub 2011 Dec 13.