Deshpande Priya N, Venkatnarayan Kavitha, Krishnaswamy Uma Maheswari, Veluthat Chitra, Niranjanmurthy Likith, Devaraj Uma, Ramachandran Priya
Department of Pulmonary Medicine St. John's National Academy of Health Sciences Bengaluru India.
Department of Radiodiagnosis St. John's National Academy of Health Sciences Bengaluru India.
Respirol Case Rep. 2024 Dec 12;12(12):e70091. doi: 10.1002/rcr2.70091. eCollection 2024 Dec.
Pulmonary artery aneurysmal rupture is a rare cause of massive hemoptysis. When the suspected origin of bleeding is the pulmonary artery, comprehensive evaluation is necessary to determine aetiology and guide appropriate management. Behçet's disease and Hughes-Stovin Syndrome (HSS) are important differentials to consider after infections and malignancy have been ruled out. Pulmonary artery aneurysms with aneurysmal wall enhancement and 'in-situ' thrombus should prompt the suspicion of HSS. Early diagnosis and treatment with immunosuppressants and endovascular interventions in selected patients may improve the prognosis and prevent episodes of fatal hemoptysis.
肺动脉瘤破裂是大量咯血的罕见原因。当怀疑出血源是肺动脉时，需要进行全面评估以确定病因并指导适当的治疗。在排除感染和恶性肿瘤后，白塞病和休斯-斯托文综合征（HSS）是需要考虑的重要鉴别诊断。伴有瘤壁强化和“原位”血栓的肺动脉瘤应引起对HSS的怀疑。对选定患者早期使用免疫抑制剂和血管内介入治疗可能会改善预后并预防致命性咯血发作。
