休斯-斯托文综合征与大量咯血：一项管理挑战。
Hughes-stovin syndrome and massive hemoptysis: a management challenge.
作者信息
Al-Zeedy Khalfan, Jayakrishnan B, Rizavi Dawar, Alkaabi Juma
机构信息
Department of Medicine, Sultan Qaboos University Hospital, Muscat, Oman.
出版信息
Oman Med J. 2015 Jan;30(1):59-62. doi: 10.5001/omj.2015.11.
Abstract
Hughes-Stovin syndrome is a very rare clinical entity characterized by pulmonary artery aneurysms and deep vein thrombosis (DVT). Here we report the case of a 53-year-old man, admitted to Sultan Qaboos University Hospital, Muscat, Oman, with bilateral pulmonary artery aneurysms and lower-limb DVT who developed massive hemoptysis. He was managed successfully with high-dose steroids in combination with cyclophosphamide.
摘要
休斯-斯托文综合征是一种非常罕见的临床病症，其特征为肺动脉瘤和深静脉血栓形成（DVT）。在此，我们报告一例53岁男性病例，该患者因双侧肺动脉瘤和下肢深静脉血栓形成入住阿曼马斯喀特的苏丹·卡布斯大学医院，随后出现大量咯血。通过大剂量类固醇联合环磷酰胺治疗，他成功康复。
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