Kumari Sandhya, Verma Ghanshyam K, Gulati Anchana, Mehta Prajul
From the Department of Dermatology, Venereology and Leprosy, Indira Gandhi Medical College Shimla, Himachal Pradesh, India.
Pathology, Indira Gandhi Medical College Shimla, Himachal Pradesh, India.
Indian J Dermatol. 2024 Nov-Dec;69(6):475-477. doi: 10.4103/ijd.ijd_633_23. Epub 2024 Oct 29.
Aggressive angiomyxoma (AA) is a very rare tumour arising from the vulvovaginal mesenchymal tissue. The literature has not reported its co-existence with hidradenitis suppurativa (HS). A 30-year-old female presented with a giant pedunculated mass arising from a scarred and disfigured perineum for 3 years. On examination, a giant mass of size 20 × 20 cm was hanging over the scarred and disfigured vulva. The clinical possibilities of AA, leiomyoma or angiomyofibroblastoma over the scars of HS were considered. The histopathological examination of the mass revealed the features of AA, and perineal lesion biopsy was suggestive of HS. The patient was managed with surgical excision of the AA along with oral antibiotics for HS.
侵袭性血管黏液瘤（AA）是一种非常罕见的起源于外阴阴道间叶组织的肿瘤。文献中尚未报道其与化脓性汗腺炎（HS）并存的情况。一名30岁女性因瘢痕累累、畸形的会阴出现巨大带蒂肿物3年前来就诊。检查时，一个大小为20×20 cm的巨大肿物悬挂在瘢痕累累、畸形的外阴上方。考虑了HS瘢痕上出现AA、平滑肌瘤或血管肌成纤维细胞瘤的临床可能性。肿物的组织病理学检查显示为AA的特征，会阴病变活检提示为HS。该患者接受了AA的手术切除以及针对HS的口服抗生素治疗。
