复发性低级别子宫内膜间质肉瘤转移至髂总静脉，12年后延伸至下腔静脉及右心房：一例报告

Recurrent Low-grade endometrial stromal sarcoma metastasized to the common iliac veins, extending into the inferior vena cava and right atrium after 12 years: A case report.

作者信息

Naaman Nour, Alyafi Mohammad, Albeshri Heitham, Jamjoom Ahmed A, AlTurkistany Samira, Al-Maghrabi Haneen, Baradwan Saeed

机构信息

Department of Obstetrics and Gynecology, King Faisal Specialist Hospital and Research Center, Jeddah, Saudi Arabia.

Department of Obstetrics and Gynecology, Faculty of Medicine, King Abdulaziz University, Jeddah, Saudi Arabia.

出版信息

Gynecol Oncol Rep. 2024 Nov 6;56:101543. doi: 10.1016/j.gore.2024.101543. eCollection 2024 Dec.

DOI:10.1016/j.gore.2024.101543

PMID:39737433

原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC11683952/

Abstract

INTRODUCTION

Extrauterine recurrent metastasis of Low-grade endometrial stromal sarcoma (LG-ESS) to major blood vessels is largely rare with few reported cases.

CASE

Herein, we present a case of a 51-year-old female with recurrent LG-ESS that has metastasized after 12 years to the inferior vena cava (IVC) and extended into the right atrium and common iliac veins. Computed tomography showed an intracardiac larger thrombus within the right atrium extending into the inferior vena cava and common iliac veins. The patient underwent cytoreduction of the intravenous tumor. Final histopathology confirmed metastatic LG-ESS. Follow-up CT scan after six months showed no residual or recurrence.

CONCLUSION

Treatment for extrauterine metastasis from LG-ESS prioritizes reducing tumor burden through surgical resection and may require collaboration across disciplines. Follow-up hormonal therapy with progestins or aromatase inhibitors significantly impacts patient prognosis.

摘要

引言

低级别子宫内膜间质肉瘤（LG-ESS）子宫外复发转移至主要血管的情况极为罕见，仅有少数病例报道。

病例

在此，我们报告一例51岁女性复发性LG-ESS病例，该病例在12年后转移至下腔静脉（IVC），并延伸至右心房和髂总静脉。计算机断层扫描显示右心房内有一个较大的心内血栓，延伸至下腔静脉和髂总静脉。患者接受了静脉肿瘤的减瘤手术。最终组织病理学证实为转移性LG-ESS。六个月后的随访CT扫描显示无残留或复发。