Morse Andrew K, Dobrila Julija, Salazar Jorge D, LaPar Damien J
Division of Pediatric Cardiac Surgery, Department of Cardiovascular Surgery, Children's Heart Institute, Children's Memorial Hermann Hospital, University of Texas Health Science Center at Houston McGovern Medical School, Houston, Texas.
Ann Thorac Surg Short Rep. 2024 Apr 16;2(3):410-413. doi: 10.1016/j.atssr.2024.03.009. eCollection 2024 Sep.
Aorticopulmonary paragangliomas are exceedingly rare tumors in pediatric populations. Complete surgical resection is the only curative treatment. However, resection is challenging due to the vascularity of paragangliomas and their close relationship with the great vessels. We present the resection of an aorticopulmonary paraganglioma that encased the main pulmonary artery bifurcation, compressed the left main coronary artery, and was densely adherent to the ascending aorta and right pulmonary artery via a median sternotomy with bypass. This case underscores the importance of complete resection for pediatric patients, despite the technical challenges.
主动脉肺副神经节瘤在儿科人群中是极其罕见的肿瘤。完整的手术切除是唯一的治愈性治疗方法。然而,由于副神经节瘤的血管丰富以及它们与大血管的密切关系,切除具有挑战性。我们报告了一例通过正中胸骨切开术并体外循环切除包裹主肺动脉分叉、压迫左主冠状动脉且与升主动脉和右肺动脉紧密粘连的主动脉肺副神经节瘤的病例。该病例强调了尽管存在技术挑战,但对儿科患者进行完整切除的重要性。