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家族性弥漫性肺骨化的肺移植

Lung Transplantation for Familial Diffuse Pulmonary Ossification.

作者信息

Ohsumi Akihiro, Yutaka Yojiro, Handa Tomohiro, Yoshizawa Akihiko, Date Hiroshi

机构信息

Department of Thoracic Surgery, Kyoto University Hospital, Kyoto, Japan.

Department of Advanced Medicine for Respiratory Failure, Kyoto University Hospital, Kyoto, Japan.

出版信息

Ann Thorac Surg Short Rep. 2024 Mar 24;2(3):495-498. doi: 10.1016/j.atssr.2024.02.015. eCollection 2024 Sep.

DOI:10.1016/j.atssr.2024.02.015
PMID:39790413
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC11708718/
Abstract

We report 3 cases of extremely rare familial idiopathic diffuse pulmonary ossification, 2 of 3 received lung transplantation and the other is listed for lung transplantation. The clinical courses of family members varied greatly, and rapid deterioration could occur; therefore, early and close examination is recommended for transplant registration. During transplantation, the lungs appeared and felt exactly like a "pumice stone" and could not collapse, and good visual field was not easily obtained. Both patients had no recurrence of pulmonary ossification for more than 2 years.

摘要

我们报告了3例极其罕见的家族性特发性弥漫性肺骨化病例，3例中有2例接受了肺移植，另一例正在等待肺移植。家庭成员的临床病程差异很大，可能会迅速恶化；因此，建议在进行移植登记时进行早期和密切检查。在移植过程中，肺部外观和触感与“浮石”完全一样，无法塌陷，且不易获得良好的视野。两名患者在超过2年的时间里均未出现肺骨化复发。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/467b/11708718/7a9461ccc06f/figs1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/467b/11708718/f7d098e7bfc3/gr1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/467b/11708718/369288840128/gr2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/467b/11708718/bdac3a02cdb0/gr3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/467b/11708718/7a9461ccc06f/figs1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/467b/11708718/f7d098e7bfc3/gr1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/467b/11708718/369288840128/gr2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/467b/11708718/bdac3a02cdb0/gr3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/467b/11708718/7a9461ccc06f/figs1.jpg

相似文献

1
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本文引用的文献

1
Nationwide retrospective observational study of idiopathic dendriform pulmonary ossification: clinical features with a progressive phenotype.全国性回顾性观察性研究：特发性树突状肺骨化：具有进行性表型的临床特征。
BMJ Open Respir Res. 2022 Sep;9(1). doi: 10.1136/bmjresp-2022-001337.
2
Lung Transplant for Pulmonary Fibrosis With Dendriform Ossification.肺纤维化伴树突状骨化的肺移植。
Ann Thorac Surg. 2022 Dec;114(6):e403-e405. doi: 10.1016/j.athoracsur.2022.01.062. Epub 2022 Feb 24.
3
Intraoperative Diagnosis of Bronchovenous Fistula During Lung Transplantation Using Transesophageal Echocardiography.
经食管超声心动图在肺移植术中诊断支气管静脉瘘。
J Cardiothorac Vasc Anesth. 2022 Aug;36(8 Pt A):2572-2574. doi: 10.1053/j.jvca.2021.09.015. Epub 2021 Sep 17.
4
Dendriform pulmonary ossification leading to bilateral lung transplant: a case report.树突状肺骨化导致双侧肺移植：病例报告。
Virchows Arch. 2018 Sep;473(3):379-383. doi: 10.1007/s00428-018-2412-3. Epub 2018 Jul 17.
5
Progressive Restrictive Ventilatory Impairment in Idiopathic Diffuse Pulmonary Ossification.特发性弥漫性肺骨化中的进行性限制性通气障碍
Intern Med. 2018 Jun 1;57(11):1631-1636. doi: 10.2169/internalmedicine.9433-17. Epub 2018 Jan 11.
6
Idiopathic dendriform pulmonary ossification.特发性树枝状肺骨化。
J Thorac Imaging. 2012 Sep;27(5):W108-10. doi: 10.1097/RTI.0b013e3182326c38.