成功修复右位心伴完全性内脏反位患者的二尖瓣和三尖瓣
Successful Mitral and Tricuspid Valve Repair for Dextrocardia With Situs Inversus Totalis.
作者信息
Kawasumi Ryo, Kainuma Satoshi, Toda Koichi, Yoshioka Daisuke, Kawamura Masashi, Saito Tetsuya, Kawamura Takuji, Matsuura Ryohei, Miyagawa Shigeru
机构信息
Department of Cardiovascular Surgery, Osaka University Graduate School of Medicine, Suita, Osaka, Japan.
出版信息
Ann Thorac Surg Short Rep. 2022 Nov 3;1(1):52-54. doi: 10.1016/j.atssr.2022.10.018. eCollection 2023 Mar.
Dextrocardia with situs inversus is a rare congenital anomaly characterized by a right-sided heart apex and inversely rotated abdominal viscera. It is often autosomal recessive and involves 1 child in every 10,000 births. We report a case of dextrocardia with situs inversus totalis in a patient who underwent mitral valve repair through an extended transseptal approach for clinically relevant mitral regurgitation secondary to Barlow disease. The operation was successfully performed without complications, and the postoperative course was uneventful.
右位心伴内脏转位是一种罕见的先天性异常，其特征为心尖位于右侧且腹部脏器呈反向旋转。它通常为常染色体隐性遗传，每10000例新生儿中约有1例患病。我们报告一例全内脏转位的右位心患者，该患者因巴洛病继发具有临床意义的二尖瓣反流，通过扩大经房间隔入路接受二尖瓣修复术。手术成功实施，无并发症发生，术后病程平稳。
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