胸腔积液、复发性支气管肺炎伴淋巴水肿、黄甲及蛋白丢失性肠病。
Pleural effusion and recurrent broncho-pneumonia with lymphedema, yellow nails and protein-losing enteropathy.
作者信息
Battaglia A, di Ricco G, Mariani G, Giuntini C
出版信息
Eur J Respir Dis. 1985 Jan;66(1):65-9.
A case is reported in whom the triad generalized lymphedema, nail dystrophy, and pleural effusion was associated to protein-losing enteropathy. This combination, not previously described, was also characterized by exacerbations of pleural effusion with recurrent episodes of broncho-pneumonia. Albumin turnover study showed depletion of the total body pool, decreased catabolic rate, and elevated albumin removal through the gastrointestinal tract. During bronchopneumonia, increased capillary permeability due to pleural involvement may worsen the basic deficit of pleural lymphatic drainage.
报道了一例三联征（全身性淋巴水肿、指甲营养不良和胸腔积液）与蛋白丢失性肠病相关的病例。这种此前未被描述过的组合还具有胸腔积液因支气管肺炎反复发作而加重的特征。白蛋白周转率研究显示全身白蛋白池减少、分解代谢率降低以及通过胃肠道的白蛋白清除增加。在支气管肺炎期间，由于胸膜受累导致的毛细血管通透性增加可能会使胸膜淋巴引流的基本缺陷恶化。
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