Fatal splenic rupture in Ehlers-Danlos syndrome.
作者信息
Harris S C, Slater D N, Austin C A
出版信息
Postgrad Med J. 1985 Mar;61(713):259-60. doi: 10.1136/pgmj.61.713.259.
Abstract
A fatal case of Ehlers-Danlos syndrome (Type IV) is described. Autopsy revealed splenic rupture that had resulted from spontaneous haemorrhage into the splenic parenchyma. This is a previously unrecorded complication of Ehlers-Danlos syndrome and should be considered in the differential diagnosis of chest and abdominal pain in patients with this condition.
摘要
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