Leaño Aljomon D, Pedregosa Bonifacio C, Villaraza Steven G, Navarro Jose C
Department of Neurology, Jose R. Reyes Memorial Medical Center, Manila, PHL.
Cureus. 2024 Dec 24;16(12):e76330. doi: 10.7759/cureus.76330. eCollection 2024 Dec.
Bilateral scapular winging is a rare and atypical manifestation of Arnold-Chiari malformation type 1 (ACM1). We report a case of ACM with extensive syrinx formation, presenting with progressive bilateral proximal upper extremity weakness, bilateral scapular winging, and segmental hypesthesia and reduced thermesthesia over the bilateral C2-C8 dermatomal levels. The patient was successfully treated with surgical decompression and syringosubarachnoid shunting. This unusual presentation of ACM1 emphasizes the need to consider central nervous system pathologies in the differential diagnosis for bilateral scapular winging.
双侧肩胛翼状肩胛是1型阿诺德-奇亚里畸形(ACM1)的一种罕见且非典型表现。我们报告一例伴有广泛空洞形成的ACM病例,其表现为双侧上肢近端进行性无力、双侧肩胛翼状肩胛,以及双侧C2 - C8皮节水平的节段性感觉减退和温度觉减退。该患者通过手术减压和空洞 - 蛛网膜下腔分流术成功治疗。ACM1的这种不寻常表现强调了在双侧肩胛翼状肩胛的鉴别诊断中需要考虑中枢神经系统病变。