Riswadkar Neha, Ramachandaran Rajoo, Pandian Nidarshana, Janarthanan Mahesh
Department of Radiology, Sri Ramachandra Institute of Higher Education, Chennai, India.
Department of Pediatrics, Sri Ramachandra Institute of Higher Education, Chennai, India.
Sudan J Paediatr. 2024;24(2):164-169. doi: 10.24911/SJP.106-1723696189.
Enthesitis related arthritis (ERA) is a specific type of juvenile idiopathic arthritis (JIA) and ERA typically begins with enthesitis and peripheral arthritis in the lower extremities, progressing later in the disease to sacroiliitis and spinal involvement. The condition has a strong relationship with the HLA-B27 and primarily affects boys between the ages of 13 and 16 years. We describe an unusual presentation of ERA in a young boy with pubic pain and fever, describing its quintessential magnetic resonance imaging (MRI) findings. A child presented to the paediatric outpatient department with fever, insidious onset pubic pain and tenderness with associated leukocytosis and elevated inflammatory markers. MRI of the pelvis revealed bilateral symmetrical bone marrow edema involving the pubic symphysis and inferior pubic rami with para symphyseal edema involving bilateral obturator externus muscle and bilateral adductor longus muscle insertions suggestive of enthesitis of the pubic symphysis. MRI also showed sacroiliitis and enthesitis at other sites. HLA-B27 was positive. The patient responded well to a short course of steroids and maintained remission with tumour necrosis factor alpha inhibitors.
附着点炎相关关节炎(ERA)是幼年特发性关节炎(JIA)的一种特殊类型,ERA通常始于附着点炎和下肢外周关节炎,在疾病后期发展为骶髂关节炎和脊柱受累。该病与HLA - B27密切相关,主要影响13至16岁的男孩。我们描述了一名患有耻骨疼痛和发热的小男孩中ERA的不寻常表现,并阐述了其典型的磁共振成像(MRI)结果。一名儿童因发热、隐匿性耻骨疼痛和压痛就诊于儿科门诊,伴有白细胞增多和炎症标志物升高。骨盆MRI显示双侧对称的骨髓水肿累及耻骨联合和耻骨下支,耻骨联合旁水肿累及双侧闭孔外肌和双侧内收长肌附着点,提示耻骨联合附着点炎。MRI还显示了其他部位的骶髂关节炎和附着点炎。HLA - B27呈阳性。该患者对短期类固醇治疗反应良好,并使用肿瘤坏死因子α抑制剂维持缓解状态。