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双孔二尖瓣:两名表现截然不同的患者。

Double Orifice Mitral Valve: Two Patients with Contrasting Presentations.

作者信息

Dey Jaideep, Bhadoriya Shailendra, Chauhan Vijay Singh, Mustaqueem Arif, Shrivastava Sameer

机构信息

Department of Cardiology, BLK-Max Super Speciality Hospital, New Delhi, India.

Department of Cardiology, Max Super Speciality Hospital, New Delhi, India.

出版信息

J Cardiovasc Echogr. 2024 Oct-Dec;34(4):222-227. doi: 10.4103/jcecho.jcecho_54_24. Epub 2024 Dec 19.

DOI:10.4103/jcecho.jcecho_54_24
PMID:39895883
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC11784732/
Abstract

Double orifice mitral valve, despite being an extremely rare entity, may be encountered on routine echocardiographic studies in adults. The varied morphology of the valve may be complicated by coexisting anomalies of the subvalvular apparatus. We present the cases of two patients with this condition and associated papillary muscle anomalies. A thorough echocardiographic study with three-dimensional imaging was pivotal in making a final diagnosis.

摘要

双孔二尖瓣尽管极为罕见,但在成人常规超声心动图检查中仍可能被发现。瓣膜形态多样,可能合并瓣下结构异常。我们报告了两例患有这种疾病及相关乳头肌异常的患者病例。采用三维成像进行全面的超声心动图检查对最终诊断至关重要。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e9d7/11784732/c60a483d4362/JCE-34-222-g012.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e9d7/11784732/2bcaf665a6c9/JCE-34-222-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e9d7/11784732/cb94e2b5a2d0/JCE-34-222-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e9d7/11784732/a525f1242a50/JCE-34-222-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e9d7/11784732/d6f9830f2a01/JCE-34-222-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e9d7/11784732/9f4d7357227f/JCE-34-222-g005.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e9d7/11784732/3d8010663e12/JCE-34-222-g006.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e9d7/11784732/8d5e130ca1d2/JCE-34-222-g007.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e9d7/11784732/c0d6dde5e087/JCE-34-222-g008.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e9d7/11784732/93c521e0bf59/JCE-34-222-g009.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e9d7/11784732/72a8c76482ed/JCE-34-222-g010.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e9d7/11784732/17b5546f52da/JCE-34-222-g011.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e9d7/11784732/c60a483d4362/JCE-34-222-g012.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e9d7/11784732/2bcaf665a6c9/JCE-34-222-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e9d7/11784732/cb94e2b5a2d0/JCE-34-222-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e9d7/11784732/a525f1242a50/JCE-34-222-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e9d7/11784732/d6f9830f2a01/JCE-34-222-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e9d7/11784732/9f4d7357227f/JCE-34-222-g005.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e9d7/11784732/3d8010663e12/JCE-34-222-g006.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e9d7/11784732/8d5e130ca1d2/JCE-34-222-g007.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e9d7/11784732/c0d6dde5e087/JCE-34-222-g008.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e9d7/11784732/93c521e0bf59/JCE-34-222-g009.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e9d7/11784732/72a8c76482ed/JCE-34-222-g010.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e9d7/11784732/17b5546f52da/JCE-34-222-g011.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e9d7/11784732/c60a483d4362/JCE-34-222-g012.jpg

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本文引用的文献

1
Atypical Shone's Complex Diagnosed at 70 Years Old: Presenting with Double-orifice Mitral Valve, Bicuspid Aortic Valve, and Aortic Coarctation.70 岁时诊断出非典型 Shone 综合征:表现为二尖瓣双孔、主动脉瓣二瓣化畸形和主动脉缩窄。
Intern Med. 2022 May 1;61(9):1367-1370. doi: 10.2169/internalmedicine.8176-21. Epub 2021 Oct 19.
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Rare Variant of Shone Complex.肖恩综合征的罕见变异型
Circ Cardiovasc Imaging. 2021 Jun;14(6):e012317. doi: 10.1161/CIRCIMAGING.120.012317. Epub 2021 May 26.
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Parachute mitral valve: Morphology and surgical management.
降落伞型二尖瓣:形态学与外科治疗
Turk Gogus Kalp Damar Cerrahisi Derg. 2020 Jan 23;28(1):219-226. doi: 10.5606/tgkdc.dergisi.2020.18041. eCollection 2020 Jan.
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Incidental finding of a double orifice mitral valve in an elderly patient: value of 3D imaging.老年患者二尖瓣双孔畸形的偶然发现:三维成像的价值
Echo Res Pract. 2017 Sep;4(3):K21-K24. doi: 10.1530/ERP-17-0023. Epub 2017 Jul 25.
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Isolated double-orifice mitral valve: a case report.孤立性双孔二尖瓣:一例报告。
BMC Cardiovasc Disord. 2015 Dec 18;15:172. doi: 10.1186/s12872-015-0168-0.
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Double-orifice mitral valve - echocardiographic findings.双孔二尖瓣-超声心动图表现。
Kardiol Pol. 2011;69(2):139-43.
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Echocardiographic diagnosis of a stenotic double orifice parachute mitral valve with a single papillary muscle.超声心动图诊断为双孔降落伞样二尖瓣狭窄伴单一乳头肌。
Echocardiography. 2000 May;17(4):349-52. doi: 10.1111/j.1540-8175.2000.tb01149.x.
8
The tensor apparatus in double-orifice mitral valve: interpretation of echocardiographic findings.双孔二尖瓣中的腱索装置:超声心动图检查结果解读
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